Giant congenital melanocytic naevus (Q39346): Difference between revisions
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Nevo melanocítico congênito (NMC) com um diâmetro máximo previsto ou final no adulto de 400 mm ou mais. NMC gigantes são comumente centrados na superfície dorsal do corpo entre o vértice e as nádegas, mas podem ocorrer em outra localização; podem estar associados a vários nevos satélites menores (congênitos ou tardios), hipertricose, lipomas ou nódulos proliferativos benignos. Existe o risco de melanoma pré-puberal no NMC gigante ou no sistema nervoso central (SNC). A melanocitose leptomeníngea ou neuromelanose focal, encontrada em 10-15% dos casos, está frequentemente associada a outros tumores do SNC, hidrocefalia, epilepsia, cistos de aracnoide ou malformação de Dandy-Walker. | |||
| description / en | description / en | ||
A congenital melanocytic naevus (CMN) with a predicted or final adult maximal diameter of 400 mm or more. Giant CMNs are commonly centred on the dorsal surface of the body between the vertex and the buttocks but may occur elsewhere; they may be associated with multiple smaller satellite naevi (congenital or tardive), hypertrichosis, lipomas or benign proliferative nodules. There is a risk of pre-pubertal melanoma within giant CMN or the central nervous system (CNS). Leptomeningeal melanocytosis or focal neuromelanosis, found in 10-15% of cases, is often associated with other CNS tumours, hydrocephalus, epilepsy, arachnoid cysts, or Dandy-Walker malformation. | |||
Revision as of 04:44, 13 August 2026
A congenital melanocytic naevus (CMN) with a predicted or final adult maximal diameter of 400 mm or more. Giant CMNs are commonly centred on the dorsal surface of the body between the vertex and the buttocks but may occur elsewhere; they may be associated with multiple smaller satellite naevi (congenital or tardive), hypertrichosis, lipomas or benign proliferative nodules. There is a risk of pre-pubertal melanoma within giant CMN or the central nervous system (CNS). Leptomeningeal melanocytosis or focal neuromelanosis, found in 10-15% of cases, is often associated with other CNS tumours, hydrocephalus, epilepsy, arachnoid cysts, or Dandy-Walker malformation.
| Language | Label | Description | Also known as |
|---|---|---|---|
| default for all languages | 2F20.20 |
||
| English | Giant congenital melanocytic naevus |
A congenital melanocytic naevus (CMN) with a predicted or final adult maximal diameter of 400 mm or more. Giant CMNs are commonly centred on the dorsal surface of the body between the vertex and the buttocks but may occur elsewhere; they may be associated with multiple smaller satellite naevi (congenital or tardive), hypertrichosis, lipomas or benign proliferative nodules. There is a risk of pre-pubertal melanoma within giant CMN or the central nervous system (CNS). Leptomeningeal melanocytosis or focal neuromelanosis, found in 10-15% of cases, is often associated with other CNS tumours, hydrocephalus, epilepsy, arachnoid cysts, or Dandy-Walker malformation. |
