Nodal marginal zone lymphoma (Q39148): Difference between revisions
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Linfoma não Hodgkin nodal primário de células B que morfologicamente se assemelha aos linfonodos envolvidos por linfomas da zona marginal dos tipos extranodal ou esplênico, mas sem evidência de doença extranodal ou esplênica. Esta é uma entidade rara, e a maioria dos pacientes apresenta linfadenopatia localizada ou generalizada. O curso clínico é indolente. | |||
| description / en | description / en | ||
A primary nodal B-cell non-Hodgkin lymphoma which morphologically resembles lymph nodes involved by marginal zone lymphomas of extranodal or splenic types, but without evidence of extranodal or splenic disease. This is a rare entity, and most patients present with localised or generalised lymphadenopathy. The clinical course is indolent. | |||
Revision as of 04:28, 13 August 2026
A primary nodal B-cell non-Hodgkin lymphoma which morphologically resembles lymph nodes involved by marginal zone lymphomas of extranodal or splenic types, but without evidence of extranodal or splenic disease. This is a rare entity, and most patients present with localised or generalised lymphadenopathy. The clinical course is indolent.
| Language | Label | Description | Also known as |
|---|---|---|---|
| default for all languages | 2A85.0 |
||
| English | Nodal marginal zone lymphoma |
A primary nodal B-cell non-Hodgkin lymphoma which morphologically resembles lymph nodes involved by marginal zone lymphomas of extranodal or splenic types, but without evidence of extranodal or splenic disease. This is a rare entity, and most patients present with localised or generalised lymphadenopathy. The clinical course is indolent. |
