Langerhans cell histiocytosis (Q39072): Difference between revisions
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Revision as of 04:23, 13 August 2026
A neoplastic proliferation of Langerhans cells which contain Birbeck granules by ultrastructural examination. Three major overlapping syndromes are recognised: eosinophilic granuloma, Letterer-Siwe disease, and Hand-Schuller-Christian disease. The clinical course is generally related to the number of organs affected at presentation.
| Language | Label | Description | Also known as |
|---|---|---|---|
| default for all languages | 2B31.2 |
||
| English | Langerhans cell histiocytosis |
A neoplastic proliferation of Langerhans cells which contain Birbeck granules by ultrastructural examination. Three major overlapping syndromes are recognised: eosinophilic granuloma, Letterer-Siwe disease, and Hand-Schuller-Christian disease. The clinical course is generally related to the number of organs affected at presentation. |
