Histiocytic necrotising lymphadenitis of Kikuchi and Fujimoto (Q105809): Difference between revisions
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Lnifadenite necrotizante histiocítica (doença de Kikuchi-Fujimoto) é uma doença rara, benigna, autolimitada, mas pouco compreendida, caracterizada por mal estar, febre, perda de peso e linfadenopatia localizada afetando particularmente os linfonodos cervicais. Outras manifestações importantes observadas em uma minoria dos casos incluem linfocipenia, uma variedade de manifestações cutâneas e uma associação com lúpus eritematoso sistêmico. A apresentação histológica característica é infiltração histiocítica e necrose de linfonodos. | |||
| description / en | description / en | ||
Histiocytic necrotizing lymphadenitis (Kikuchi-Fujimoto disease) is a rare benign, self-limited but poorly understood disease characterised by malaise, fever, weight loss and localised lymphadenopathy affecting particularly cervical lymph nodes. Other important features found in a minority of cases include lymphocytopenia, a variety of skin manifestations and an association with systemic lupus erythematosus. The histological hallmark is histiocytic infiltration and necrosis of lymph nodes. | |||
Revision as of 12:17, 17 August 2026
Histiocytic necrotizing lymphadenitis (Kikuchi-Fujimoto disease) is a rare benign, self-limited but poorly understood disease characterised by malaise, fever, weight loss and localised lymphadenopathy affecting particularly cervical lymph nodes. Other important features found in a minority of cases include lymphocytopenia, a variety of skin manifestations and an association with systemic lupus erythematosus. The histological hallmark is histiocytic infiltration and necrosis of lymph nodes.
| Language | Label | Description | Also known as |
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| default for all languages | ID_2087666237 |
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| English | Histiocytic necrotising lymphadenitis of Kikuchi and Fujimoto |
Histiocytic necrotizing lymphadenitis (Kikuchi-Fujimoto disease) is a rare benign, self-limited but poorly understood disease characterised by malaise, fever, weight loss and localised lymphadenopathy affecting particularly cervical lymph nodes. Other important features found in a minority of cases include lymphocytopenia, a variety of skin manifestations and an association with systemic lupus erythematosus. The histological hallmark is histiocytic infiltration and necrosis of lymph nodes. |
