Myelinoclastic diffuse sclerosis (Q105511): Difference between revisions

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Transtorno desmielinizante caracterizado por inflamação e uma lesão ampla, ou lesões, de destruição mielínica. Esclerose difusa é um transtorno raro caracterizado por uma placa de desmielinização inflamatória da substância branca, que frequentemente simula uma neoplasia ou abcesso intracraniano. Usualmente afeta crianças enre 5 a 14 anos de idade. Caracteriza-se por uma ou duas lesões dispostas simetricamente, medindo pelo menos 2 x 3 cm, com envolvimento do centro semioval no cenário de sintomas incomuns para esclerose múltipla.
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This is a demyelinating disorder characterised by inflammation and a large lesion, or lesions, of myelin destruction. Diffuse sclerosis is a rare disorder characterised by an inflammatory white matter plaque of demyelination, which often mimics intracranial neoplasm or abscess. It usually affects children between 5 and 14 years old . Characterised by a single or two symmetrically arranged lesions measuring at least 2 x 3cm with involvement of the centrum semiovale in the setting of symptoms unusual for multiple sclerosis.

Revision as of 11:49, 17 August 2026

This is a demyelinating disorder characterised by inflammation and a large lesion, or lesions, of myelin destruction. Diffuse sclerosis is a rare disorder characterised by an inflammatory white matter plaque of demyelination, which often mimics intracranial neoplasm or abscess. It usually affects children between 5 and 14 years old . Characterised by a single or two symmetrically arranged lesions measuring at least 2 x 3cm with involvement of the centrum semiovale in the setting of symptoms unusual for multiple sclerosis.
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ID_816172167
    English
    Myelinoclastic diffuse sclerosis
    This is a demyelinating disorder characterised by inflammation and a large lesion, or lesions, of myelin destruction. Diffuse sclerosis is a rare disorder characterised by an inflammatory white matter plaque of demyelination, which often mimics intracranial neoplasm or abscess. It usually affects children between 5 and 14 years old . Characterised by a single or two symmetrically arranged lesions measuring at least 2 x 3cm with involvement of the centrum semiovale in the setting of symptoms unusual for multiple sclerosis.

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