Isolated mitochondrial respiratory chain complex IV deficiency (Q102292): Difference between revisions

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Trata-se de transferência de elétrons acoplada isolada entre um doador de elétrons (como NADH) e um receptor/ aceptor de elétrons (como O2) com a transferência de íons H + (prótons) através de uma membrana. Esse diagnóstico é com deficiência do Complexo IV, com quatro elétrons sendo retirados de quatro moléculas do citocromo e transferidos para o oxigênio molecular (O2), produzindo duas moléculas de água.
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This refers to isolated coupled electron transfer between an electron donor (such as NADH) and an electron acceptor (such as O2) with the transfer of H+ ions (protons) across a membrane. This diagnosis is with deficiency in Complex IV, with four electrons being removed from four molecules of cytochrome c and transferred to molecular oxygen (O2), producing two molecules of water.

Revision as of 19:13, 16 August 2026

This refers to isolated coupled electron transfer between an electron donor (such as NADH) and an electron acceptor (such as O2) with the transfer of H+ ions (protons) across a membrane. This diagnosis is with deficiency in Complex IV, with four electrons being removed from four molecules of cytochrome c and transferred to molecular oxygen (O2), producing two molecules of water.
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ID_1247726031
    English
    Isolated mitochondrial respiratory chain complex IV deficiency
    This refers to isolated coupled electron transfer between an electron donor (such as NADH) and an electron acceptor (such as O2) with the transfer of H+ ions (protons) across a membrane. This diagnosis is with deficiency in Complex IV, with four electrons being removed from four molecules of cytochrome c and transferred to molecular oxygen (O2), producing two molecules of water.

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