Isolated mitochondrial respiratory chain complex IV deficiency (Q102292): Difference between revisions
From determinar.ia.br - Determine suas informações
Created a new Item |
Changed label, description and/or aliases in pt-br, en |
||
| description / pt-br | description / pt-br | ||
Trata-se de transferência de elétrons acoplada isolada entre um doador de elétrons (como NADH) e um receptor/ aceptor de elétrons (como O2) com a transferência de íons H + (prótons) através de uma membrana. Esse diagnóstico é com deficiência do Complexo IV, com quatro elétrons sendo retirados de quatro moléculas do citocromo e transferidos para o oxigênio molecular (O2), produzindo duas moléculas de água. | |||
| description / en | description / en | ||
This refers to isolated coupled electron transfer between an electron donor (such as NADH) and an electron acceptor (such as O2) with the transfer of H+ ions (protons) across a membrane. This diagnosis is with deficiency in Complex IV, with four electrons being removed from four molecules of cytochrome c and transferred to molecular oxygen (O2), producing two molecules of water. | |||
Revision as of 19:13, 16 August 2026
This refers to isolated coupled electron transfer between an electron donor (such as NADH) and an electron acceptor (such as O2) with the transfer of H+ ions (protons) across a membrane. This diagnosis is with deficiency in Complex IV, with four electrons being removed from four molecules of cytochrome c and transferred to molecular oxygen (O2), producing two molecules of water.
| Language | Label | Description | Also known as |
|---|---|---|---|
| default for all languages | ID_1247726031 |
||
| English | Isolated mitochondrial respiratory chain complex IV deficiency |
This refers to isolated coupled electron transfer between an electron donor (such as NADH) and an electron acceptor (such as O2) with the transfer of H+ ions (protons) across a membrane. This diagnosis is with deficiency in Complex IV, with four electrons being removed from four molecules of cytochrome c and transferred to molecular oxygen (O2), producing two molecules of water. |
