Infantile bilateral striatal necrosis (Q101723): Difference between revisions
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A necrose estriatal bilateral infantil (NEBI) compreende várias síndromes de degeneração esponjosa simétrica bilateral do núcleo caudado, putâmen e globo pálido, caracterizada por regressão do desenvolvimento, coreoatetose e distonia progredindo para quadriparesia espástica. NEBI pode ser familiar ou esporádica. | |||
| description / en | description / en | ||
Infantile bilateral striatal necrosis (IBSN) comprises several syndromes of bilateral symmetric spongy degeneration of the caudate nucleus, putamen and globus pallidus characterised by developmental regression, choreoathetosis and dystonia progressing to spastic quadriparesis. IBSN can be familial or sporadic. | |||
Revision as of 18:34, 16 August 2026
Infantile bilateral striatal necrosis (IBSN) comprises several syndromes of bilateral symmetric spongy degeneration of the caudate nucleus, putamen and globus pallidus characterised by developmental regression, choreoathetosis and dystonia progressing to spastic quadriparesis. IBSN can be familial or sporadic.
| Language | Label | Description | Also known as |
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| default for all languages | ID_1947032348 |
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| English | Infantile bilateral striatal necrosis |
Infantile bilateral striatal necrosis (IBSN) comprises several syndromes of bilateral symmetric spongy degeneration of the caudate nucleus, putamen and globus pallidus characterised by developmental regression, choreoathetosis and dystonia progressing to spastic quadriparesis. IBSN can be familial or sporadic. |
