Mercedes Benz pattern craniosynostosis (Q99675): Difference between revisions

From determinar.ia.br - Determine suas informações
‎Created a new Item
 
‎Changed label, description and/or aliases in pt-br, en
description / pt-brdescription / pt-br
 
Descreve uma condição de craniossinostose de suturas sagital e lambdoides bilaterais, não associada a outras características (a síndrome de Mercedes Benz é um termo que leva a engano). A vista posterior mostra a estrutura trirradiada característica de suturas fundidas. A expansão compensatória leva à protuberância frontal, mimetizando a sinostose coronal. A inteligência é normal, mas a incidência de pressão intracraniana elevada é maior.
description / endescription / en
 
Describes a condition of craniosynostosis of sagittal and bilateral lambdoid sutures, not associated with other features (Mercedes Benz syndrome is a misleading term). Posterior view shows characteristic triradiate structure of fused sutures. Compensatory expansion leads to frontal bossing, mimicking coronal synostosis. Intelligence is normal but the incidence of raised intracranial pressure is higher.

Revision as of 16:21, 16 August 2026

Describes a condition of craniosynostosis of sagittal and bilateral lambdoid sutures, not associated with other features (Mercedes Benz syndrome is a misleading term). Posterior view shows characteristic triradiate structure of fused sutures. Compensatory expansion leads to frontal bossing, mimicking coronal synostosis. Intelligence is normal but the incidence of raised intracranial pressure is higher.
Language Label Description Also known as
default for all languages
ID_1349730024
    English
    Mercedes Benz pattern craniosynostosis
    Describes a condition of craniosynostosis of sagittal and bilateral lambdoid sutures, not associated with other features (Mercedes Benz syndrome is a misleading term). Posterior view shows characteristic triradiate structure of fused sutures. Compensatory expansion leads to frontal bossing, mimicking coronal synostosis. Intelligence is normal but the incidence of raised intracranial pressure is higher.

      Statements