Multicentric carpotarsal osteolysis - nephropathy (Q98290): Difference between revisions
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A osteólise multicêntrica idiopática é uma síndrome muito rara caracterizada por perda progressiva de osso, geralmente os ossos do carpo e do tarso, resultando em deformidade e incapacidade. A insuficiência renal crônica ocorre em muitos casos. Os distúrbios ósseos e renais, às vezes, estão associados a déficit intelectual e anormalidades faciais. | |||
| description / en | description / en | ||
Idiopathic multicentric osteolysis is a very rare syndrome characterised by progressive loss of bone, usually the carpal and tarsal bones, resulting in deformity and disability, as well as chronic renal failure in many cases. The bone and renal disorders are sometimes associated with intellectual deficit and facial abnormalities. | |||
Revision as of 14:41, 16 August 2026
Idiopathic multicentric osteolysis is a very rare syndrome characterised by progressive loss of bone, usually the carpal and tarsal bones, resulting in deformity and disability, as well as chronic renal failure in many cases. The bone and renal disorders are sometimes associated with intellectual deficit and facial abnormalities.
| Language | Label | Description | Also known as |
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| default for all languages | ID_1675573486 |
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| English | Multicentric carpotarsal osteolysis - nephropathy |
Idiopathic multicentric osteolysis is a very rare syndrome characterised by progressive loss of bone, usually the carpal and tarsal bones, resulting in deformity and disability, as well as chronic renal failure in many cases. The bone and renal disorders are sometimes associated with intellectual deficit and facial abnormalities. |
