Erythrokeratodermia variabilis et progressiva (Q94074): Difference between revisions

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A eritroqueratodermia variável do tipo Mendes da Costa (EKV) é uma genodermatose caracterizada pelo aparecimento de duas lesões cutâneas independentes: manchas eritematosas figuradas transitórias e hiperceratose que é geralmente localizada, mas ocasionalmente ocorre em sua forma generalizada, geralmente durante o primeiro ano de vida.
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Mendes da Costa type erythrokeratodermia variabilis (EKV) is a genodermatosis characterised by the appearance of two independent skin lesions: transient figurate erythematous patches and hyperkeratosis that is usually localised but occasionally occurs in its generalised form, generally during the first year of life.

Revision as of 09:11, 16 August 2026

Mendes da Costa type erythrokeratodermia variabilis (EKV) is a genodermatosis characterised by the appearance of two independent skin lesions: transient figurate erythematous patches and hyperkeratosis that is usually localised but occasionally occurs in its generalised form, generally during the first year of life.
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ID_886266813
    English
    Erythrokeratodermia variabilis et progressiva
    Mendes da Costa type erythrokeratodermia variabilis (EKV) is a genodermatosis characterised by the appearance of two independent skin lesions: transient figurate erythematous patches and hyperkeratosis that is usually localised but occasionally occurs in its generalised form, generally during the first year of life.

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