Bernard-Soulier syndrome (Q93445): Difference between revisions
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A síndrome de Bernard-Soulier, também conhecida como distrofia trombocítica hemorragípara, é um distúrbio hemorrágico hereditário que afeta a linhagem de megacariócitos/plaquetas e é caracterizada por tendência hemorrágica, plaquetas gigantes no sangue e contagens plaquetárias baixas. | |||
| description / en | description / en | ||
Bernard-Soulier Syndrome, also known as haemorrhagiparous thrombocytic dystrophy, is a hereditary bleeding disorder affecting the megakaryocyte/platelet lineage and characterised by bleeding tendency, giant blood platelets and low platelet counts. | |||
Revision as of 08:33, 16 August 2026
Bernard-Soulier Syndrome, also known as haemorrhagiparous thrombocytic dystrophy, is a hereditary bleeding disorder affecting the megakaryocyte/platelet lineage and characterised by bleeding tendency, giant blood platelets and low platelet counts.
| Language | Label | Description | Also known as |
|---|---|---|---|
| default for all languages | ID_507309898 |
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| English | Bernard-Soulier syndrome |
Bernard-Soulier Syndrome, also known as haemorrhagiparous thrombocytic dystrophy, is a hereditary bleeding disorder affecting the megakaryocyte/platelet lineage and characterised by bleeding tendency, giant blood platelets and low platelet counts. |
