Epidermolysis bullosa acquisita, Brunsting-Perry type (Q85876): Difference between revisions
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A variante Brunsting-Perry da epidermólise bolhosa adquirida é uma rara doença mecanobolhosa autoimune da pele caracterizada por bolhas e cicatrizes da pele facial ou do couro cabeludo e pela presença de autoanticorpos IgG contra a fibrila de ancoragem da membrana basal, colágeno VII. Isso a distingue da variante de Brunsting-Perry, que é clinicamente semelhante ao penfigóide cítrico, na qual esse anticorpo não é encontrado. | |||
| description / en | description / en | ||
The Brunsting-Perry variant of epidermolysis bullosa acquisita is a rare mechanobullous autoimmune skin disease characterised by blistering and scarring of facial or scalp skin and the presence of IgG autoantibodies to the basement membrane anchoring fibril, collagen VII. This distinguishes it from the clinically similar Brunsting-Perry variant of cictricial pemphigoid in which this antibody is not found. | |||
Revision as of 11:14, 15 August 2026
The Brunsting-Perry variant of epidermolysis bullosa acquisita is a rare mechanobullous autoimmune skin disease characterised by blistering and scarring of facial or scalp skin and the presence of IgG autoantibodies to the basement membrane anchoring fibril, collagen VII. This distinguishes it from the clinically similar Brunsting-Perry variant of cictricial pemphigoid in which this antibody is not found.
| Language | Label | Description | Also known as |
|---|---|---|---|
| default for all languages | ID_1417911502 |
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| English | Epidermolysis bullosa acquisita, Brunsting-Perry type |
The Brunsting-Perry variant of epidermolysis bullosa acquisita is a rare mechanobullous autoimmune skin disease characterised by blistering and scarring of facial or scalp skin and the presence of IgG autoantibodies to the basement membrane anchoring fibril, collagen VII. This distinguishes it from the clinically similar Brunsting-Perry variant of cictricial pemphigoid in which this antibody is not found. |
