Von Willebrand disease type 1 (Q84138): Difference between revisions
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A doença de von Willebrand (DVW) tipo 1 é um tipo de DVW (veja este termo) caracterizada por um transtorno hemorrágico associado a uma deficiência plasmática quantitativa parcial de um fator de von Willebrand (FVW) estruturalmente e funcionalmente normal se não fosse por essa alteração. A doença do tipo 1 é considerada a forma mais comum de DVW, respondendo por entre 50% e 75% dos casos, embora sua prevalência esteja provavelmente subestimada. A idade à apresentação do sangramento anormal varia, estando a manifestação precoce e sintomas mais graves associados com deficiências mais graves do FVW. | |||
| description / en | description / en | ||
Type 1 von Willebrand disease (type 1 VWD) is a form of VWD (see this term) characterised by a bleeding disorder associated with a partial quantitative plasmatic deficiency of an otherwise structurally and functionally normal Willebrand factor (von Willebrand factor; VWF). The type 1 disease is considered to be the most common form of VWD, accounting for between 50 and 75% of cases but its prevalence is probably overestimated. Age of onset of bleeding anomalies varies, with earlier onset and more severe symptoms being associated with more severe VWF deficiency. | |||
Revision as of 09:30, 15 August 2026
Type 1 von Willebrand disease (type 1 VWD) is a form of VWD (see this term) characterised by a bleeding disorder associated with a partial quantitative plasmatic deficiency of an otherwise structurally and functionally normal Willebrand factor (von Willebrand factor; VWF). The type 1 disease is considered to be the most common form of VWD, accounting for between 50 and 75% of cases but its prevalence is probably overestimated. Age of onset of bleeding anomalies varies, with earlier onset and more severe symptoms being associated with more severe VWF deficiency.
| Language | Label | Description | Also known as |
|---|---|---|---|
| default for all languages | ID_1861858008 |
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| English | Von Willebrand disease type 1 |
Type 1 von Willebrand disease (type 1 VWD) is a form of VWD (see this term) characterised by a bleeding disorder associated with a partial quantitative plasmatic deficiency of an otherwise structurally and functionally normal Willebrand factor (von Willebrand factor; VWF). The type 1 disease is considered to be the most common form of VWD, accounting for between 50 and 75% of cases but its prevalence is probably overestimated. Age of onset of bleeding anomalies varies, with earlier onset and more severe symptoms being associated with more severe VWF deficiency. |
