Microdontia - microtia type I - deafness (Q64618): Difference between revisions
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Surdez com aplasia labiríntica, microtia e microdontia (LAMM) é uma síndrome de surdez de transmissão genética. em que a surdez congênita profunda está associada a uma ausência completa de estruturas da orelha interna (aplasia de Michel); microtia tipo I com aurícula pequena e conduto auditivo externo estreito; e microdontia com dentes amplamente espaçados. | |||
| description / en | description / en | ||
Deafness with labyrinthine aplasia, microtia, and microdontia (LAMM) is a genetic transmission deafness syndrome. in which the profound congenital deafness is associated with a complete absence of inner ear structures (Michel aplasia); microtia type I with small auricle and narrow external auditory canal; and microdontia with widely spaced teeth. | |||
Revision as of 12:19, 14 August 2026
Deafness with labyrinthine aplasia, microtia, and microdontia (LAMM) is a genetic transmission deafness syndrome. in which the profound congenital deafness is associated with a complete absence of inner ear structures (Michel aplasia); microtia type I with small auricle and narrow external auditory canal; and microdontia with widely spaced teeth.
| Language | Label | Description | Also known as |
|---|---|---|---|
| default for all languages | ID_1619903146 |
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| English | Microdontia - microtia type I - deafness |
Deafness with labyrinthine aplasia, microtia, and microdontia (LAMM) is a genetic transmission deafness syndrome. in which the profound congenital deafness is associated with a complete absence of inner ear structures (Michel aplasia); microtia type I with small auricle and narrow external auditory canal; and microdontia with widely spaced teeth. |
