Progressive supranuclear palsy (Q49441): Difference between revisions
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Paralisia supranuclear progressiva (PSP) é uma doença neurodegenerativa de início tardio caracterizada por paralisia supranuclear do olhar, instabilidade postural, rigidez progressiva e demência leve. Foram descritas cinco variantes clínicas com correlações clinicopatológicas: PSP clássica (Síndrome de Richardson) e quatro variantes atípicas de PSP, incluindo PSP-parkinsonismo (PSP-P), PSP-Acinesia pura com congelamento de marcha (PSP-PAGF), PSP-Síndrome corticobasal (PSP-SCB) e PSP - Afasia progressiva não fluente (PSP-PNFA). | |||
| description / en | description / en | ||
Progressive supranuclear palsy (PSP) is a late-onset neurodegenerative disease characterised by supranuclear gaze palsy, postural instability, progressive rigidity, and mild dementia. Five clinical variants have been described with clinicopathological correlations: Classical PSP (Richardson's syndrome), and four atypical variants of PSP including PSP-Parkinsonism (PSP-P), PSP-Pure akinesia with gait freezing (PSP-PAGF), PSP-corticobasal syndrome (PSP-CBS), and PSP-progressive non fluent aphasia (PSP-PNFA). | |||
Revision as of 19:49, 13 August 2026
Progressive supranuclear palsy (PSP) is a late-onset neurodegenerative disease characterised by supranuclear gaze palsy, postural instability, progressive rigidity, and mild dementia. Five clinical variants have been described with clinicopathological correlations: Classical PSP (Richardson's syndrome), and four atypical variants of PSP including PSP-Parkinsonism (PSP-P), PSP-Pure akinesia with gait freezing (PSP-PAGF), PSP-corticobasal syndrome (PSP-CBS), and PSP-progressive non fluent aphasia (PSP-PNFA).
| Language | Label | Description | Also known as |
|---|---|---|---|
| default for all languages | 8A00.10 |
||
| English | Progressive supranuclear palsy |
Progressive supranuclear palsy (PSP) is a late-onset neurodegenerative disease characterised by supranuclear gaze palsy, postural instability, progressive rigidity, and mild dementia. Five clinical variants have been described with clinicopathological correlations: Classical PSP (Richardson's syndrome), and four atypical variants of PSP including PSP-Parkinsonism (PSP-P), PSP-Pure akinesia with gait freezing (PSP-PAGF), PSP-corticobasal syndrome (PSP-CBS), and PSP-progressive non fluent aphasia (PSP-PNFA). |
