Ebstein malformation of tricuspid valve (Q46184): Difference between revisions
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Malformação cardiovascular congênita da valva tricúspide e do ventrículo direito, caracterizada pela laminação incompleta dos folhetos valvares tricúspide septal e inferior (posterior) a partir do miocárdio do ventrículo direito, e graus variáveis de deslocamento rotacional para baixo (apical) do anel funcional ._x000D_ _x000D_ Informações adicionais: as anomalias cardíacas associadas incluem comunicação interatrial, a presença de vias de condução acessórias e graus variáveis de obstrução da via de saída do ventrículo direito, incluindo atresia pulmonar. No cenário de conexões atrioventriculares e ventrículo-arteriais discordantes ["Transposição das grandes artérias corrigida congenitamente"], "malformação de Ebstein da valva tricúspide" pode estar presente. | |||
| description / en | description / en | ||
A congenital cardiovascular malformation of the tricuspid valve and right ventricle that is characterised by incomplete delamination of the septal and inferior (posterior) tricuspid valvar leaflets from the myocardium of the right ventricle, and varying degrees of downward (apical) rotational displacement of the functional annulus. Additional information: associated cardiac anomalies include an interatrial communication, the presence of accessory conduction pathways and varying degrees of right ventricular outflow tract obstruction, including pulmonary atresia. In the setting of discordant atrioventricular and ventriculo-arterial connections ['Congenitally corrected transposition of great arteries'], 'Ebstein malformation of tricuspid valve' may be present. | |||
Revision as of 14:36, 13 August 2026
A congenital cardiovascular malformation of the tricuspid valve and right ventricle that is characterised by incomplete delamination of the septal and inferior (posterior) tricuspid valvar leaflets from the myocardium of the right ventricle, and varying degrees of downward (apical) rotational displacement of the functional annulus. Additional information: associated cardiac anomalies include an interatrial communication, the presence of accessory conduction pathways and varying degrees of right ventricular outflow tract obstruction, including pulmonary atresia. In the setting of discordant atrioventricular and ventriculo-arterial connections ['Congenitally corrected transposition of great arteries'], 'Ebstein malformation of tricuspid valve' may be present.
| Language | Label | Description | Also known as |
|---|---|---|---|
| default for all languages | LA87.03 |
||
| English | Ebstein malformation of tricuspid valve |
A congenital cardiovascular malformation of the tricuspid valve and right ventricle that is characterised by incomplete delamination of the septal and inferior (posterior) tricuspid valvar leaflets from the myocardium of the right ventricle, and varying degrees of downward (apical) rotational displacement of the functional annulus. Additional information: associated cardiac anomalies include an interatrial communication, the presence of accessory conduction pathways and varying degrees of right ventricular outflow tract obstruction, including pulmonary atresia. In the setting of discordant atrioventricular and ventriculo-arterial connections ['Congenitally corrected transposition of great arteries'], 'Ebstein malformation of tricuspid valve' may be present. |
