Pulmonary alveolar proteinosis (Q42933): Difference between revisions
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| description / pt-br | description / pt-br | ||
Doença pulmonar rara em que ocorre acúmulo anormal de surfactante dentro dos alvéolos, interferindo com a troca gasosa. A PAP pode ocorrer de forma primária ou secundária no contexto de malignidades (especialmente na leucemia mieloide), infecção pulmonar ou exposição ambiental a poeiras ou substâncias químicas. | |||
| description / en | description / en | ||
This is a rare lung disease in which abnormal accumulation of surfactant occurs within the alveoli, interfering with gas exchange. PAP can occur in a primary form or secondarily in the settings of malignancy (especially in myeloid leukemia), pulmonary infection, or environmental exposure to dusts or chemicals. | |||
Revision as of 09:41, 13 August 2026
This is a rare lung disease in which abnormal accumulation of surfactant occurs within the alveoli, interfering with gas exchange. PAP can occur in a primary form or secondarily in the settings of malignancy (especially in myeloid leukemia), pulmonary infection, or environmental exposure to dusts or chemicals.
| Language | Label | Description | Also known as |
|---|---|---|---|
| default for all languages | CB04.31 |
||
| English | Pulmonary alveolar proteinosis |
This is a rare lung disease in which abnormal accumulation of surfactant occurs within the alveoli, interfering with gas exchange. PAP can occur in a primary form or secondarily in the settings of malignancy (especially in myeloid leukemia), pulmonary infection, or environmental exposure to dusts or chemicals. |
