Endocardial fibroelastosis (Q42361): Difference between revisions

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A fibroelastose endocárdica é a formação de um acentuado espessamento fibroelástico do subendocárdio em um ou ambos os ventrículos cardíacos. Um transtorno de fetos e bebês, as causas secundárias incluem lesões cardíacas obstrutivas congênitas do lado esquerdo, distúrbios metabólicos, doença autoimune (anticorpos anti-Ro/anti-La) e infecção viral transplacentária, como caxumba. A fibroelastose endocárdica primária tem sido associada à herança recessiva e ligada ao X, como na síndrome de Barth.
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Endocardial fibroelastosis is the formation of a marked fibro-elastic thickening of the subendocardium in one or both cardiac ventricles. A disorder of fetuses and infants, secondary causes include congenital left-sided obstructive cardiac lesions, metabolic disorders, autoimmune disease (anti-Ro/anti-La antibodies), and transplacental viral infection such as mumps. Primary endocardial fibroelastosis has been linked to recessive and x-linked inheritance, such as with Barth syndrome.

Revision as of 08:50, 13 August 2026

Endocardial fibroelastosis is the formation of a marked fibro-elastic thickening of the subendocardium in one or both cardiac ventricles. A disorder of fetuses and infants, secondary causes include congenital left-sided obstructive cardiac lesions, metabolic disorders, autoimmune disease (anti-Ro/anti-La antibodies), and transplacental viral infection such as mumps. Primary endocardial fibroelastosis has been linked to recessive and x-linked inheritance, such as with Barth syndrome.
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BC43.3
    English
    Endocardial fibroelastosis
    Endocardial fibroelastosis is the formation of a marked fibro-elastic thickening of the subendocardium in one or both cardiac ventricles. A disorder of fetuses and infants, secondary causes include congenital left-sided obstructive cardiac lesions, metabolic disorders, autoimmune disease (anti-Ro/anti-La antibodies), and transplacental viral infection such as mumps. Primary endocardial fibroelastosis has been linked to recessive and x-linked inheritance, such as with Barth syndrome.

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