Progressive muscular atrophy (Q41051): Difference between revisions
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Na atrofia muscular progressiva, os sinais do neurônio motor inferior em músculos de membros e tronco estão presentes sem envolvimento do neurônio motor superior. Com o tempo, alguns pacientes podem progredir para desenvolver sinais do neurônio motor superior, dos quais a evidência patológica é comum mesmo em pacientes que nunca apresentaram sinais clínicos do neurônio motor superior, sugerindo que a atrofia muscular progressiva é uma forma de ELA. | |||
| description / en | description / en | ||
In progressive muscular atrophy, lower motor neuron signs in limb and trunk muscles are present without upper motor neuron involvement. Over time, some patients may progress to develop upper motor neuron signs, of which pathological evidence is common even in patients who never displayed clinical upper motor neuron signs, suggesting that progressive muscular atrophy is a form of ALS. | |||
Revision as of 07:06, 13 August 2026
In progressive muscular atrophy, lower motor neuron signs in limb and trunk muscles are present without upper motor neuron involvement. Over time, some patients may progress to develop upper motor neuron signs, of which pathological evidence is common even in patients who never displayed clinical upper motor neuron signs, suggesting that progressive muscular atrophy is a form of ALS.
| Language | Label | Description | Also known as |
|---|---|---|---|
| default for all languages | 8B60.3 |
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| English | Progressive muscular atrophy |
In progressive muscular atrophy, lower motor neuron signs in limb and trunk muscles are present without upper motor neuron involvement. Over time, some patients may progress to develop upper motor neuron signs, of which pathological evidence is common even in patients who never displayed clinical upper motor neuron signs, suggesting that progressive muscular atrophy is a form of ALS. |
