Pituitary-dependent Cushing disease (Q39856): Difference between revisions
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Doença de Cushing é causada por um tumor hipofisário, geralmente benigno (adenoma) raramente maligno (carcinoma), que secreta adrenocorticotrofina autonomamente, levando ao hipercortisolismo. Essa condição esta associada com aumento da morbidade e mortalidade que pode ser mitigada por tratamentos que resultem em remissão endócrina sustentada. Cirurgia transesfenoidal (CTS) é o principal tratamento para a doença mas requer considerável conhecimento neurocirúrgico e experiência para otimizar os resultados dos pacientes. | |||
| description / en | description / en | ||
Pituitary-dependent Cushing disease is caused by a pituitary tumour, generally benign (adenoma) but rarely malignant (carcinoma), which secretes adrenocorticotropin (ACTH) autonomously, leading to hypercortisolism. The condition is associated with increased morbidity and mortality that can be mitigated by treatments that result in sustained endocrine remission. Transsphenoidal pituitary surgery (TSS) remains the mainstay of treatment for this disease but requires considerable neurosurgical expertise and experience in order to optimize patient outcomes. | |||
Revision as of 05:25, 13 August 2026
Pituitary-dependent Cushing disease is caused by a pituitary tumour, generally benign (adenoma) but rarely malignant (carcinoma), which secretes adrenocorticotropin (ACTH) autonomously, leading to hypercortisolism. The condition is associated with increased morbidity and mortality that can be mitigated by treatments that result in sustained endocrine remission. Transsphenoidal pituitary surgery (TSS) remains the mainstay of treatment for this disease but requires considerable neurosurgical expertise and experience in order to optimize patient outcomes.
| Language | Label | Description | Also known as |
|---|---|---|---|
| default for all languages | 5A70.0 |
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| English | Pituitary-dependent Cushing disease |
Pituitary-dependent Cushing disease is caused by a pituitary tumour, generally benign (adenoma) but rarely malignant (carcinoma), which secretes adrenocorticotropin (ACTH) autonomously, leading to hypercortisolism. The condition is associated with increased morbidity and mortality that can be mitigated by treatments that result in sustained endocrine remission. Transsphenoidal pituitary surgery (TSS) remains the mainstay of treatment for this disease but requires considerable neurosurgical expertise and experience in order to optimize patient outcomes. |
