Hepatic veno-occlusive disease - immunodeficiency syndrome (Q39734): Difference between revisions
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Doença hepática veno-oclusiva - síndrome de imunodeficiência caracterizada pela associação de hipogamaglobulinemia grave, imunodeficiência combinada de células T e B, ausência de centros germinativos linfonodais, ausência de plasmócitos teciduais e doença veno-oclusiva hepática. | |||
| description / en | description / en | ||
Hepatic veno-occlusive disease - immunodeficiency syndrome is characterised by the association of severe hypogammaglobulinemia, combined T and B cell immunodeficiency, absent lymph node germinal centres, absent tissue plasma cells and hepatic veno-occlusive disease. | |||
Revision as of 05:15, 13 August 2026
Hepatic veno-occlusive disease - immunodeficiency syndrome is characterised by the association of severe hypogammaglobulinemia, combined T and B cell immunodeficiency, absent lymph node germinal centres, absent tissue plasma cells and hepatic veno-occlusive disease.
| Language | Label | Description | Also known as |
|---|---|---|---|
| default for all languages | 4A01.33 |
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| English | Hepatic veno-occlusive disease - immunodeficiency syndrome |
Hepatic veno-occlusive disease - immunodeficiency syndrome is characterised by the association of severe hypogammaglobulinemia, combined T and B cell immunodeficiency, absent lymph node germinal centres, absent tissue plasma cells and hepatic veno-occlusive disease. |
