Severe combined immunodeficiencies (Q39699): Difference between revisions
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Imunodeficiência combinada grave (IDCG) compreende um grupo de transtornos raros de imunodeficiência primária monogênica caracterizados pela ausência de linfócitos T periféricos funcionais, resultando em infecções respiratórias graves de início precoce e déficit de crescimento. | |||
| description / en | description / en | ||
Severe combined immunodeficiency (SCID) comprises a group of rare monogenic primary immunodeficiency disorders characterised by a lack of functional peripheral T lymphocytes resulting in early-onset severe respiratory infections and failure to thrive. | |||
Revision as of 05:13, 13 August 2026
Severe combined immunodeficiency (SCID) comprises a group of rare monogenic primary immunodeficiency disorders characterised by a lack of functional peripheral T lymphocytes resulting in early-onset severe respiratory infections and failure to thrive.
| Language | Label | Description | Also known as |
|---|---|---|---|
| default for all languages | 4A01.10 |
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| English | Severe combined immunodeficiencies |
Severe combined immunodeficiency (SCID) comprises a group of rare monogenic primary immunodeficiency disorders characterised by a lack of functional peripheral T lymphocytes resulting in early-onset severe respiratory infections and failure to thrive. |
