Beta thalassaemia (Q39517): Difference between revisions

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A talassemia beta (BT) é uma hemoglobinopatia caracterizada por deficiência (Beta+) ou ausência (Beta0) da síntese das cadeias de beta globina da hemoglobina (Hb). Foram descritos três tipos principais da BT: menor, intermédia e maior com apresentação clínica variando de formas assintomáticas a anemia microcítica e esplenomegalia devido a eritropoiese defeituosa e hemólise.
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Beta-thalassemia (BT) is a haemoglobinopathy characterised by deficiency (Beta+) or absence (Beta0) of synthesis of the beta globin chains of haemoglobin (Hb). Three main types of BT have been described: minor, intermedia and major with clinical presentation ranging from asymptomatic forms to microcytic anaemia and splenomegaly due to defective erythropoiesis and haemolysis.

Revision as of 04:57, 13 August 2026

Beta-thalassemia (BT) is a haemoglobinopathy characterised by deficiency (Beta+) or absence (Beta0) of synthesis of the beta globin chains of haemoglobin (Hb). Three main types of BT have been described: minor, intermedia and major with clinical presentation ranging from asymptomatic forms to microcytic anaemia and splenomegaly due to defective erythropoiesis and haemolysis.
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3A50.2
    English
    Beta thalassaemia
    Beta-thalassemia (BT) is a haemoglobinopathy characterised by deficiency (Beta+) or absence (Beta0) of synthesis of the beta globin chains of haemoglobin (Hb). Three main types of BT have been described: minor, intermedia and major with clinical presentation ranging from asymptomatic forms to microcytic anaemia and splenomegaly due to defective erythropoiesis and haemolysis.

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