Cutaneous mastocytosis (Q39214): Difference between revisions

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A mastocitose cutânea é caracterizada pelo acúmulo e proliferação anormais de mastócitos cutâneos. A maioria dos tipos é isolada, mas a mastocitose cutânea pode ocorrer em associação com doença sistêmica. As formas clínicas incluem mastocitoma cutâneo, urticária pigmentosa (a forma mais frequente), mastocitose cutânea nodular pseudoxantomatosa, telangiectasia macular eruptiva perstans e mastocitose cutânea difusa.
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Cutaneous mastocytosis is characterised by abnormal accumulation and proliferation of cutaneous mast cells. Most types are isolated but cutaneous mastocytosis can occur in association with systemic disease. Clinical forms include cutaneous mastocytoma, urticaria pigmentosa (the most frequent form), pseudoxanthomatous nodular cutaneous mastocytosis, telangiectasia macularis eruptiva perstans and diffuse cutaneous mastocytosis.

Revision as of 04:33, 13 August 2026

Cutaneous mastocytosis is characterised by abnormal accumulation and proliferation of cutaneous mast cells. Most types are isolated but cutaneous mastocytosis can occur in association with systemic disease. Clinical forms include cutaneous mastocytoma, urticaria pigmentosa (the most frequent form), pseudoxanthomatous nodular cutaneous mastocytosis, telangiectasia macularis eruptiva perstans and diffuse cutaneous mastocytosis.
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2A21.1
    English
    Cutaneous mastocytosis
    Cutaneous mastocytosis is characterised by abnormal accumulation and proliferation of cutaneous mast cells. Most types are isolated but cutaneous mastocytosis can occur in association with systemic disease. Clinical forms include cutaneous mastocytoma, urticaria pigmentosa (the most frequent form), pseudoxanthomatous nodular cutaneous mastocytosis, telangiectasia macularis eruptiva perstans and diffuse cutaneous mastocytosis.

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