Gamma heavy chain disease (Q39153): Difference between revisions

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Transtorno clonal caracterizado pela secreção de uma cadeia gama truncada. Na maioria dos casos, está associada a alterações morfológicas também observadas em linfomas linfoplasmocitários, mas o curso clínico é tipicamente mais agressivo do que no linfoma linfoplasmocitário/macroglobulinemia de Waldenström.
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A clonal disorder characterised by the secretion of a truncated gamma chain. In most cases, it is associated with morphologic changes also seen in lymphoplasmacytic lymphomas, but the clinical course is typically more aggressive than in lymphoplasmacytic lymphoma/Waldenstrom's macroglobulinemia.

Revision as of 04:28, 13 August 2026

A clonal disorder characterised by the secretion of a truncated gamma chain. In most cases, it is associated with morphologic changes also seen in lymphoplasmacytic lymphomas, but the clinical course is typically more aggressive than in lymphoplasmacytic lymphoma/Waldenstrom's macroglobulinemia.
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2A84.1
    English
    Gamma heavy chain disease
    A clonal disorder characterised by the secretion of a truncated gamma chain. In most cases, it is associated with morphologic changes also seen in lymphoplasmacytic lymphomas, but the clinical course is typically more aggressive than in lymphoplasmacytic lymphoma/Waldenstrom's macroglobulinemia.

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