Haemoglobinopathy-associated acquired pseudoxanthoma elasticum (Q105185): Difference between revisions
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O pseudoxantoma elástico adquirido associado a hemoglobinopatia tem sido associado a uma variedade de hemoglobinopatias, incluindo anemia falciforme, beta talassemia e esferocitose hereditária. As manifestações clínicas são semelhantes à da forma genética, mas de gravidade variável e geralmente de início tardio. A patogênese não é completamente compreendida. | |||||||||||||||
| description / en | description / en | ||||||||||||||
Haemoglobinopathy-associated acquired pseudoxanthoma elasticum has been associated with a variety of haemoglobinopathies including sickle cell anaemia, beta-thalassaemia and hereditary spherocytosis. Clinical manifestations are similar to the genetic form but of variable severity and generally of late onset. The pathogenesis is not fully understood. | |||||||||||||||
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| Property / Canonical URI: https://id.who.int/icd/entity/1336740058 / rank | |||||||||||||||
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CID11:ID_1336740058 | |||||||||||||||
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dki-india-ID_1336740058 | |||||||||||||||
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| Property / Verification Status: Concluído / rank | |||||||||||||||
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| Property / Knowledge Architect: https://pauloleads.com.br/cases-publicos/ / rank | |||||||||||||||
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16 August 2026
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| Property / Collection date: 16 August 2026 / rank | |||||||||||||||
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Latest revision as of 11:13, 17 August 2026
Haemoglobinopathy-associated acquired pseudoxanthoma elasticum has been associated with a variety of haemoglobinopathies including sickle cell anaemia, beta-thalassaemia and hereditary spherocytosis. Clinical manifestations are similar to the genetic form but of variable severity and generally of late onset. The pathogenesis is not fully understood.
| Language | Label | Description | Also known as |
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| default for all languages | ID_1336740058 |
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| English | Haemoglobinopathy-associated acquired pseudoxanthoma elasticum |
Haemoglobinopathy-associated acquired pseudoxanthoma elasticum has been associated with a variety of haemoglobinopathies including sickle cell anaemia, beta-thalassaemia and hereditary spherocytosis. Clinical manifestations are similar to the genetic form but of variable severity and generally of late onset. The pathogenesis is not fully understood. |
Statements
CID11:ID_1336740058
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dki-india-ID_1336740058
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Concluído
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16 August 2026
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