Pityriasis rubra pilaris type V, atypical juvenile (Q96878): Difference between revisions

@@ description / pt-br / description / pt-br @@
+Essa forma infantil crônica de pitiríase rubra pilar é incomum e provavelmente geneticamente heterogênea. Pode estar presente ao nascimento ou começar na primeira infância com eritema generalizado e hiperqueratose. A hiperqueratose folicular é uma característica proeminente e a ceratodermia é comum. Alterações semelhantes à esclerodermia foram descritas nas mãos e nos pés.
@@ description / en / description / en @@
+This chronic childhood form of pityriasis rubra pilaris is uncommon and probably genetically heterogeneous. It may be present at birth or start in early childhood with widespread erythema and hyperkeratosis. Follicular hyperkeratosis is a prominent feature and keratoderma is common. Scleroderma-like changes have been described in the hands and feet.
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+https://id.who.int/icd/entity/178883706
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@@ Property / CURIE @@
+CID11:ID_178883706
@@ Property / CURIE: CID11:ID_178883706 / rank @@
+Normal rank
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+dki-india-ID_178883706
@@ Property / Canary Token: dki-india-ID_178883706 / rank @@
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@@ Property / Verification Status @@
+Concluído
@@ Property / Verification Status: Concluído / rank @@
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@@ Property / Knowledge Architect @@
+https://pauloleads.com.br/cases-publicos/
+Normal rank
@@ Property / Collection date @@
+August 2026Timestamp +2026-08-15T00:00:00Z
Timezone +00:00
Calendar Gregorian
Precision 1 day
Before 0
After 0
-Timestamp
++2026-08-15T00:00:00Z
-Timezone
++00:00
-Calendar
+Gregorian
-Precision
+day
 Before
 After
@@ Property / Collection date: 15 August 2026 / rank @@
+Normal rank

Latest revision as of 12:54, 16 August 2026

This chronic childhood form of pityriasis rubra pilaris is uncommon and probably genetically heterogeneous. It may be present at birth or start in early childhood with widespread erythema and hyperkeratosis. Follicular hyperkeratosis is a prominent feature and keratoderma is common. Scleroderma-like changes have been described in the hands and feet.

Language	Label	Description	Also known as
default for all languages	ID_178883706
English	Pityriasis rubra pilaris type V, atypical juvenile	This chronic childhood form of pityriasis rubra pilaris is uncommon and probably genetically heterogeneous. It may be present at birth or start in early childhood with widespread erythema and hyperkeratosis. Follicular hyperkeratosis is a prominent feature and keratoderma is common. Scleroderma-like changes have been described in the hands and feet.