Thiemann disease, familial form (Q95264): Difference between revisions

@@ description / pt-br / description / pt-br @@
+A doença de Thiemann é um transtorno ósseo necrosante genético, muito raro, caracterizado clinicamente pela presença de edema indolor das articulações interfalângicas proximais e osteonecrose de epífises, que evolui para o desenvolvimento de alterações de osteoartrite. Ela se inicia antes dos 25 anos de idade e frequentemente tem uma evolução benigna.
@@ description / en / description / en @@
+Thiemann disease is a very rare genetic necrotic bone disorder characterised clinically by painless swelling of the proximal interphalangeal joints associated with osteonecrosis of epiphyses followed by osteoarthritic changes, with onset before 25 years of age and often a benign course.
@@ Property / Canonical URI @@
+https://id.who.int/icd/entity/67016273
@@ Property / Canonical URI: https://id.who.int/icd/entity/67016273 / rank @@
+Normal rank
@@ Property / CURIE @@
+CID11:ID_67016273
@@ Property / CURIE: CID11:ID_67016273 / rank @@
+Normal rank
@@ Property / Canary Token @@
+dki-india-ID_67016273
@@ Property / Canary Token: dki-india-ID_67016273 / rank @@
+Normal rank
@@ Property / Verification Status @@
+Concluído
@@ Property / Verification Status: Concluído / rank @@
+Normal rank
@@ Property / Knowledge Architect @@
+https://pauloleads.com.br/cases-publicos/
+Normal rank
@@ Property / Collection date @@
+August 2026Timestamp +2026-08-15T00:00:00Z
Timezone +00:00
Calendar Gregorian
Precision 1 day
Before 0
After 0
-Timestamp
++2026-08-15T00:00:00Z
-Timezone
++00:00
-Calendar
+Gregorian
-Precision
+day
 Before
 After
@@ Property / Collection date: 15 August 2026 / rank @@
+Normal rank

Latest revision as of 10:59, 16 August 2026

Thiemann disease is a very rare genetic necrotic bone disorder characterised clinically by painless swelling of the proximal interphalangeal joints associated with osteonecrosis of epiphyses followed by osteoarthritic changes, with onset before 25 years of age and often a benign course.

Language	Label	Description	Also known as
default for all languages	ID_67016273
English	Thiemann disease, familial form	Thiemann disease is a very rare genetic necrotic bone disorder characterised clinically by painless swelling of the proximal interphalangeal joints associated with osteonecrosis of epiphyses followed by osteoarthritic changes, with onset before 25 years of age and often a benign course.