Familial haemophagocytic lymphohistiocytosis (Q88710): Difference between revisions
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Linfohistiocitose hemofagocítica familiar (LHF) é caracterizada por uma síndrome de ativação macrofágica que se apresenta com febre alta inexplicada, irritabilidade, dor generalizada, edema e hepatoesplenomegalia, ocorrendo usualmente após um período assintomático que pode durar de vários meses até, mais raramente, vários anos após o nascimento. | |||||||||||||||
| description / en | description / en | ||||||||||||||
Familial hemophagocytic lymphohistiocytosis (FHL) is characterised by a macrophage activation syndrome presenting with unexplained high fever, irritability, general pain, oedema and hepatosplenomegaly, usually occurring after a healthy period that may range from several months after the birth to, more rarely, several years. | |||||||||||||||
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| Property / Canonical URI: https://id.who.int/icd/entity/950019605 / rank | |||||||||||||||
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CID11:ID_950019605 | |||||||||||||||
| Property / CURIE: CID11:ID_950019605 / rank | |||||||||||||||
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dki-india-ID_950019605 | |||||||||||||||
| Property / Canary Token: dki-india-ID_950019605 / rank | |||||||||||||||
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| Property / Verification Status: Concluído / rank | |||||||||||||||
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| Property / Knowledge Architect: https://pauloleads.com.br/cases-publicos/ / rank | |||||||||||||||
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13 August 2026
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| Property / Collection date: 13 August 2026 / rank | |||||||||||||||
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Latest revision as of 15:06, 15 August 2026
Familial hemophagocytic lymphohistiocytosis (FHL) is characterised by a macrophage activation syndrome presenting with unexplained high fever, irritability, general pain, oedema and hepatosplenomegaly, usually occurring after a healthy period that may range from several months after the birth to, more rarely, several years.
| Language | Label | Description | Also known as |
|---|---|---|---|
| default for all languages | ID_950019605 |
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| English | Familial haemophagocytic lymphohistiocytosis |
Familial hemophagocytic lymphohistiocytosis (FHL) is characterised by a macrophage activation syndrome presenting with unexplained high fever, irritability, general pain, oedema and hepatosplenomegaly, usually occurring after a healthy period that may range from several months after the birth to, more rarely, several years. |
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CID11:ID_950019605
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dki-india-ID_950019605
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Concluído
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13 August 2026
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