Von Willebrand disease type 3 (Q84143): Difference between revisions
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A doença de von Willebrand (DVW) tipo 3 é a forma mais grave de DVW, caracterizada por um transtorno hemorrágico associado a uma ausência total ou quase total de fator de von Willebrand (FVW) no plasma e nos compartimentos celulares, levando também a uma deficiência profunda do fator VIII plasmático. A doença do tipo 3 constitui a forma mais rara de DVW, respondendo por menos de 5% de todos os casos. | |||||||||||||||
| description / en | description / en | ||||||||||||||
Type 3 von Willebrand disease is the most severe form of VWD characterised by a bleeding disorder associated with a total or near-total absence of Willebrand factor (von Willebrand factor; VWF) in the plasma and cellular compartments, also leading to a profound deficiency of plasmatic factor VIII (FVIII). The type 3 disease is the rarest form of VWD, accounting for less than 5% of all cases. | |||||||||||||||
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| Property / Canonical URI: https://id.who.int/icd/entity/805917536 / rank | |||||||||||||||
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CID11:ID_805917536 | |||||||||||||||
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dki-india-ID_805917536 | |||||||||||||||
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| Property / Knowledge Architect: https://pauloleads.com.br/cases-publicos/ / rank | |||||||||||||||
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13 August 2026
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| Property / Collection date: 13 August 2026 / rank | |||||||||||||||
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Latest revision as of 09:30, 15 August 2026
Type 3 von Willebrand disease is the most severe form of VWD characterised by a bleeding disorder associated with a total or near-total absence of Willebrand factor (von Willebrand factor; VWF) in the plasma and cellular compartments, also leading to a profound deficiency of plasmatic factor VIII (FVIII). The type 3 disease is the rarest form of VWD, accounting for less than 5% of all cases.
| Language | Label | Description | Also known as |
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| default for all languages | ID_805917536 |
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| English | Von Willebrand disease type 3 |
Type 3 von Willebrand disease is the most severe form of VWD characterised by a bleeding disorder associated with a total or near-total absence of Willebrand factor (von Willebrand factor; VWF) in the plasma and cellular compartments, also leading to a profound deficiency of plasmatic factor VIII (FVIII). The type 3 disease is the rarest form of VWD, accounting for less than 5% of all cases. |
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CID11:ID_805917536
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dki-india-ID_805917536
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Concluído
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13 August 2026
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