Congenital supravalvar aortic stenosis (Q46226): Difference between revisions

@@ description / pt-br / description / pt-br @@
+Malformação cardiovascular congênita com estreitamento da aorta ao nível da junção sinotubular, que pode se estender até a aorta ascendente._x000D_ _x000D_ Informações adicionais: 'Estenose aórtica supravalvar congênita' é descrita como três formas: uma deformidade em ampulheta, uma membrana fibrosa e um estreitamento difuso da aorta ascendente. A estenose aórtica supravalvar pode envolver os óstios das artérias coronárias e os folhetos aórticos podem estar fixados. As artérias coronárias podem se tornar tortuosas e dilatadas devido a pressões elevadas e pode ocorrer aterosclerose precoce.
@@ description / en / description / en @@
+A congenital cardiovascular malformation with narrowing of the aorta at the level of the sinotubular junction which may extend into the ascending aorta. Additional information: 'Congenital supravalvar aortic stenosis' is described as three forms: an hourglass deformity, a fibrous membrane, and a diffuse narrowing of the ascending aorta. Supravalvar aortic stenosis may involve the coronary artery ostia, and the aortic leaflets may be tethered. The coronary arteries can become tortuous and dilated due to elevated pressures and early atherosclerosis may ensue.
@@ Property / Canonical URI @@
+https://id.who.int/icd/entity/1066595728
@@ Property / Canonical URI: https://id.who.int/icd/entity/1066595728 / rank @@
+Normal rank
@@ Property / CURIE @@
+CID11:LA8A.3
@@ Property / CURIE: CID11:LA8A.3 / rank @@
+Normal rank
@@ Property / Canary Token @@
+dki-india-LA8A.3
@@ Property / Canary Token: dki-india-LA8A.3 / rank @@
+Normal rank
@@ Property / Verification Status @@
+Concluído
@@ Property / Verification Status: Concluído / rank @@
+Normal rank
@@ Property / Knowledge Architect @@
+https://pauloleads.com.br/cases-publicos/
+Normal rank
@@ Property / Collection date @@
+August 2026Timestamp +2026-08-13T00:00:00Z
Timezone +00:00
Calendar Gregorian
Precision 1 day
Before 0
After 0
-Timestamp
++2026-08-13T00:00:00Z
-Timezone
++00:00
-Calendar
+Gregorian
-Precision
+day
 Before
 After
@@ Property / Collection date: 13 August 2026 / rank @@
+Normal rank
@@ Property / Linked ICD 10 @@
+Q25.3
@@ Property / Linked ICD 10: Q25.3 / rank @@
+Normal rank

Latest revision as of 14:40, 13 August 2026

A congenital cardiovascular malformation with narrowing of the aorta at the level of the sinotubular junction which may extend into the ascending aorta. Additional information: 'Congenital supravalvar aortic stenosis' is described as three forms: an hourglass deformity, a fibrous membrane, and a diffuse narrowing of the ascending aorta. Supravalvar aortic stenosis may involve the coronary artery ostia, and the aortic leaflets may be tethered. The coronary arteries can become tortuous and dilated due to elevated pressures and early atherosclerosis may ensue.

Language	Label	Description	Also known as
default for all languages	LA8A.3
English	Congenital supravalvar aortic stenosis	A congenital cardiovascular malformation with narrowing of the aorta at the level of the sinotubular junction which may extend into the ascending aorta. Additional information: 'Congenital supravalvar aortic stenosis' is described as three forms: an hourglass deformity, a fibrous membrane, and a diffuse narrowing of the ascending aorta. Supravalvar aortic stenosis may involve the coronary artery ostia, and the aortic leaflets may be tethered. The coronary arteries can become tortuous and dilated due to elevated pressures and early atherosclerosis may ensue.