IgG4 related disease (Q44401): Difference between revisions

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A síndrome relacionada a IgG4 (doença relacionada a IgG4: IgG4-RD) é uma doença clínica caracterizada por concentração sérica elevada de IgG4 e tumefação ou infiltração tecidual por plasmócitos IgG4 positivas. Os critérios diagnósticos para a síndrome relacionada à IgG4 foram propostos e podem estar presentes em uma determinada população de pacientes com uma ampla variedade de doenças, incluindo doença de Mikulicz, pancreatite autoimune, hipofisite, tireoidite de Riedel, pneumonite intersticial, nefrite intersticial, prostatite, linfadenopatia , fibrose retroperitoneal, aneurisma inflamatório da aorta e pseudotumor inflamatório.
description / endescription / en
 
IgG4 related syndrome (IgG4-related disease: IgG4-RD) is a clinical disease characterised by elevated serum IgG4 concentration and tumefaction or tissue infiltration by IgG4-positive plasma cells. The diagnostic criteria for IgG4 related syndrome have been proposed, and it may be present in a certain population of patients with a wide variety of diseases, including Mikulicz disease, autoimmune pancreatitis, hypophysitis, Riedel thyroiditis, interstitial pneumonitis, interstitial nephritis, prostatitis, lymphadenopathy, retroperitoneal fibrosis, inflammatory aortic aneurysm, and inflammatory pseudo tumour.
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Property / Canonical URI: https://id.who.int/icd/entity/99883782 / rank
 
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CID11:4A43.0
Property / CURIE: CID11:4A43.0 / rank
 
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dki-india-4A43.0
Property / Canary Token: dki-india-4A43.0 / rank
 
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Concluído
Property / Verification Status: Concluído / rank
 
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Property / Knowledge Architect
 
Property / Knowledge Architect: https://pauloleads.com.br/cases-publicos/ / rank
 
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13 August 2026
Timestamp+2026-08-13T00:00:00Z
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CalendarGregorian
Precision1 day
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Property / Collection date: 13 August 2026 / rank
 
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Property / Linked ICD 10: M35.8 / rank
 
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Latest revision as of 11:51, 13 August 2026

IgG4 related syndrome (IgG4-related disease: IgG4-RD) is a clinical disease characterised by elevated serum IgG4 concentration and tumefaction or tissue infiltration by IgG4-positive plasma cells. The diagnostic criteria for IgG4 related syndrome have been proposed, and it may be present in a certain population of patients with a wide variety of diseases, including Mikulicz disease, autoimmune pancreatitis, hypophysitis, Riedel thyroiditis, interstitial pneumonitis, interstitial nephritis, prostatitis, lymphadenopathy, retroperitoneal fibrosis, inflammatory aortic aneurysm, and inflammatory pseudo tumour.
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4A43.0
    English
    IgG4 related disease
    IgG4 related syndrome (IgG4-related disease: IgG4-RD) is a clinical disease characterised by elevated serum IgG4 concentration and tumefaction or tissue infiltration by IgG4-positive plasma cells. The diagnostic criteria for IgG4 related syndrome have been proposed, and it may be present in a certain population of patients with a wide variety of diseases, including Mikulicz disease, autoimmune pancreatitis, hypophysitis, Riedel thyroiditis, interstitial pneumonitis, interstitial nephritis, prostatitis, lymphadenopathy, retroperitoneal fibrosis, inflammatory aortic aneurysm, and inflammatory pseudo tumour.

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      CID11:4A43.0
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      dki-india-4A43.0
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      Concluído
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      13 August 2026
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