Idiopathic pulmonary fibrosis (Q42939): Difference between revisions

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Fibrose pulmonar idiopática (FPI) é definida como uma forma específica de pneumonia (pneumonite) intersticial crônica progressiva de causa desconhecida, que ocorre principalmente em adultos mais velhos, limitada aos pulmões e associada a padrão histopatológico e/ou radiológico de PIU (pneumonia intersticial usual). A definição de FPI requer a exclusão de outras formas de pneumonia (pneumonite) intersticial, incluindo outras pneumonias (pneumonites) intersticiais idiopáticas e Doença Intersticial Pulmonar (DIP) associada a exposição ambiental, medicação ou doença sistêmica.
description / endescription / en
 
Idiopathic pulmonary fibrosis (IPF) is defined as a specific form of chronic, progressive fibrosing interstitial pneumonia (pneumonitis) of unknown cause, occurring primarily in older adults, limited to the lungs, and associated with the histopathologic and/or radiologic pattern of UIP (Usual Interstitial Pneumonia). The definition of IPF requires the exclusion of other forms of interstitial pneumonia (pneumonitis) including other idiopathic interstitial pneumonias (pneumonitis) and Interstitial Lung Disease (ILD) associated with environmental exposure, medication, or systemic disease.
Property / Canonical URI
 
Property / Canonical URI: https://id.who.int/icd/entity/1074069640 / rank
 
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Property / CURIE
 
CID11:CB03.4
Property / CURIE: CID11:CB03.4 / rank
 
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Property / Canary Token
 
dki-india-CB03.4
Property / Canary Token: dki-india-CB03.4 / rank
 
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Concluído
Property / Verification Status: Concluído / rank
 
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Property / Knowledge Architect
 
Property / Knowledge Architect: https://pauloleads.com.br/cases-publicos/ / rank
 
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Property / Collection date
 
13 August 2026
Timestamp+2026-08-13T00:00:00Z
Timezone+00:00
CalendarGregorian
Precision1 day
Before0
After0
Property / Collection date: 13 August 2026 / rank
 
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Property / Linked ICD 10
 
Property / Linked ICD 10: J84.1 / rank
 
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Latest revision as of 09:42, 13 August 2026

Idiopathic pulmonary fibrosis (IPF) is defined as a specific form of chronic, progressive fibrosing interstitial pneumonia (pneumonitis) of unknown cause, occurring primarily in older adults, limited to the lungs, and associated with the histopathologic and/or radiologic pattern of UIP (Usual Interstitial Pneumonia). The definition of IPF requires the exclusion of other forms of interstitial pneumonia (pneumonitis) including other idiopathic interstitial pneumonias (pneumonitis) and Interstitial Lung Disease (ILD) associated with environmental exposure, medication, or systemic disease.
Language Label Description Also known as
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CB03.4
    English
    Idiopathic pulmonary fibrosis
    Idiopathic pulmonary fibrosis (IPF) is defined as a specific form of chronic, progressive fibrosing interstitial pneumonia (pneumonitis) of unknown cause, occurring primarily in older adults, limited to the lungs, and associated with the histopathologic and/or radiologic pattern of UIP (Usual Interstitial Pneumonia). The definition of IPF requires the exclusion of other forms of interstitial pneumonia (pneumonitis) including other idiopathic interstitial pneumonias (pneumonitis) and Interstitial Lung Disease (ILD) associated with environmental exposure, medication, or systemic disease.

      Statements

      CID11:CB03.4
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      dki-india-CB03.4
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      Concluído
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      13 August 2026
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