Arrhythmogenic ventricular cardiomyopathy (Q42308): Difference between revisions

@@ description / pt-br / description / pt-br @@
+A cardiomiopatia ventricular arritmogênica é uma cardiomiopatia caracterizada pela perda de células miocárdicas com substituição parcial ou total do músculo ventricular direito por tecido adiposo e fibroso, começando pelo subepicárdio e se tornando transmural com o tempo, poupando os músculos papilares e trabéculas, e frequentemente associada a aneurismas, particularmente da via de saída ventricular direita. Há comprometimento sistólico progressivo com dilatação ventricular e acentuada propensão a arritmias ventriculares de origem ventricular direita, e também esquerda. Classicamente uma doença do ventrículo direito, evidências mais recentes sugerem envolvimento do ventrículo esquerdo em extensão variável em até 75% dos casos, assim como doença isolada do ventrículo esquerdo.
@@ description / en / description / en @@
+Arrhythmogenic ventricular cardiomyopathy is a cardiomyopathy characterised by myocardial cell loss with partial or total replacement of right ventricular muscle by adipose and fibrous tissue, beginning subepicardially to become transmural in time, sparing the papillary muscles and trabeculae, and often associated with aneurysms particularly of the right ventricular outflow tract. There is progressive systolic impairment with ventricular dilation and marked propensity for ventricular arrhythmias of right, as well as left, ventricular origin. Classically a disease of the right ventricle, more recent evidence suggests left ventricular involvement to a varying extent in up to 75% of cases, as well as isolated left ventricular disease.
@@ Property / Canonical URI @@
+https://id.who.int/icd/entity/702771512
@@ Property / Canonical URI: https://id.who.int/icd/entity/702771512 / rank @@
+Normal rank
@@ Property / CURIE @@
+CID11:BC43.6
@@ Property / CURIE: CID11:BC43.6 / rank @@
+Normal rank
@@ Property / Canary Token @@
+dki-india-BC43.6
@@ Property / Canary Token: dki-india-BC43.6 / rank @@
+Normal rank
@@ Property / Verification Status @@
+Concluído
@@ Property / Verification Status: Concluído / rank @@
+Normal rank
@@ Property / Knowledge Architect @@
+https://pauloleads.com.br/cases-publicos/
+Normal rank
@@ Property / Collection date @@
+August 2026Timestamp +2026-08-13T00:00:00Z
Timezone +00:00
Calendar Gregorian
Precision 1 day
Before 0
After 0
-Timestamp
++2026-08-13T00:00:00Z
-Timezone
++00:00
-Calendar
+Gregorian
-Precision
+day
 Before
 After
@@ Property / Collection date: 13 August 2026 / rank @@
+Normal rank
@@ Property / Linked ICD 10 @@
+I30-I52
@@ Property / Linked ICD 10: I30-I52 / rank @@
+Normal rank

Latest revision as of 08:45, 13 August 2026

Arrhythmogenic ventricular cardiomyopathy is a cardiomyopathy characterised by myocardial cell loss with partial or total replacement of right ventricular muscle by adipose and fibrous tissue, beginning subepicardially to become transmural in time, sparing the papillary muscles and trabeculae, and often associated with aneurysms particularly of the right ventricular outflow tract. There is progressive systolic impairment with ventricular dilation and marked propensity for ventricular arrhythmias of right, as well as left, ventricular origin. Classically a disease of the right ventricle, more recent evidence suggests left ventricular involvement to a varying extent in up to 75% of cases, as well as isolated left ventricular disease.

Language	Label	Description	Also known as
default for all languages	BC43.6
English	Arrhythmogenic ventricular cardiomyopathy	Arrhythmogenic ventricular cardiomyopathy is a cardiomyopathy characterised by myocardial cell loss with partial or total replacement of right ventricular muscle by adipose and fibrous tissue, beginning subepicardially to become transmural in time, sparing the papillary muscles and trabeculae, and often associated with aneurysms particularly of the right ventricular outflow tract. There is progressive systolic impairment with ventricular dilation and marked propensity for ventricular arrhythmias of right, as well as left, ventricular origin. Classically a disease of the right ventricle, more recent evidence suggests left ventricular involvement to a varying extent in up to 75% of cases, as well as isolated left ventricular disease.