Pituitary-dependent Cushing disease (Q39856): Difference between revisions

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Doença de Cushing é causada por um tumor hipofisário, geralmente benigno (adenoma) raramente maligno (carcinoma), que secreta adrenocorticotrofina autonomamente, levando ao hipercortisolismo. Essa condição esta associada com aumento da morbidade e mortalidade que pode ser mitigada por tratamentos que resultem em remissão endócrina sustentada. Cirurgia transesfenoidal (CTS) é o principal tratamento para a doença mas requer considerável conhecimento neurocirúrgico e experiência para otimizar os resultados dos pacientes.
description / endescription / en
 
Pituitary-dependent Cushing disease is caused by a pituitary tumour, generally benign (adenoma) but rarely malignant (carcinoma), which secretes adrenocorticotropin (ACTH) autonomously, leading to hypercortisolism. The condition is associated with increased morbidity and mortality that can be mitigated by treatments that result in sustained endocrine remission. Transsphenoidal pituitary surgery (TSS) remains the mainstay of treatment for this disease but requires considerable neurosurgical expertise and experience in order to optimize patient outcomes.
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Property / Canonical URI: https://id.who.int/icd/entity/380861892 / rank
 
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Property / CURIE
 
CID11:5A70.0
Property / CURIE: CID11:5A70.0 / rank
 
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Property / Canary Token
 
dki-india-5A70.0
Property / Canary Token: dki-india-5A70.0 / rank
 
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Concluído
Property / Verification Status: Concluído / rank
 
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Property / Knowledge Architect
 
Property / Knowledge Architect: https://pauloleads.com.br/cases-publicos/ / rank
 
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Property / Collection date
 
13 August 2026
Timestamp+2026-08-13T00:00:00Z
Timezone+00:00
CalendarGregorian
Precision1 day
Before0
After0
Property / Collection date: 13 August 2026 / rank
 
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Property / Linked ICD 10
 
Property / Linked ICD 10: E24.0 / rank
 
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Latest revision as of 05:25, 13 August 2026

Pituitary-dependent Cushing disease is caused by a pituitary tumour, generally benign (adenoma) but rarely malignant (carcinoma), which secretes adrenocorticotropin (ACTH) autonomously, leading to hypercortisolism. The condition is associated with increased morbidity and mortality that can be mitigated by treatments that result in sustained endocrine remission. Transsphenoidal pituitary surgery (TSS) remains the mainstay of treatment for this disease but requires considerable neurosurgical expertise and experience in order to optimize patient outcomes.
Language Label Description Also known as
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5A70.0
    English
    Pituitary-dependent Cushing disease
    Pituitary-dependent Cushing disease is caused by a pituitary tumour, generally benign (adenoma) but rarely malignant (carcinoma), which secretes adrenocorticotropin (ACTH) autonomously, leading to hypercortisolism. The condition is associated with increased morbidity and mortality that can be mitigated by treatments that result in sustained endocrine remission. Transsphenoidal pituitary surgery (TSS) remains the mainstay of treatment for this disease but requires considerable neurosurgical expertise and experience in order to optimize patient outcomes.

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      CID11:5A70.0
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      dki-india-5A70.0
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      Concluído
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      13 August 2026
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