Hereditary deficiency of factor I (Q39582): Difference between revisions

@@ description / pt-br / description / pt-br @@
+Deficiências congênitas do fibrinogênio são distúrbios da coagulação caracterizados por manifestações hemorrágicas que variam de leves a graves, como resultado da quantidade e/ou qualidade reduzida de fibrinogênio circulante. Afibrinogenemia (ausência completa de fibrinogênio) e hipofibrinogenemia (concentração plasmática reduzida de fibrinogênio) correspondem a anomalias quantitativas do fibrinogênio, enquanto disfibrinogenemia corresponde a uma anomalia funcional do fibrinogênio. Hipo- e disfribinogenemia podem, frequentemente, coexistir (hipodisfribrinogenemia).
@@ description / en / description / en @@
+Congenital deficiencies of fibrinogen are coagulation disorders characterised by bleeding symptoms ranging from mild to severe resulting from reduced quantity and/or quality of circulating fibrinogen. Afibrinogenaemia (complete absence of fibrinogen) and hypofibrinogenaemia (reduced plasma fibrinogen concentration) correspond to quantitative anomalies of fibrinogen while dysfibrinogenaemia corresponds to a functional anomaly of fibrinogen. Hypo- and dysfibrinogenaemia may be frequently combined (hypodysfibrinogenaemia).
@@ Property / Canonical URI @@
+https://id.who.int/icd/entity/1452989457
@@ Property / Canonical URI: https://id.who.int/icd/entity/1452989457 / rank @@
+Normal rank
@@ Property / CURIE @@
+CID11:3B14.0
@@ Property / CURIE: CID11:3B14.0 / rank @@
+Normal rank
@@ Property / Canary Token @@
+dki-india-3B14.0
@@ Property / Canary Token: dki-india-3B14.0 / rank @@
+Normal rank
@@ Property / Verification Status @@
+Concluído
@@ Property / Verification Status: Concluído / rank @@
+Normal rank
@@ Property / Knowledge Architect @@
+https://pauloleads.com.br/cases-publicos/
+Normal rank
@@ Property / Collection date @@
+August 2026Timestamp +2026-08-13T00:00:00Z
Timezone +00:00
Calendar Gregorian
Precision 1 day
Before 0
After 0
-Timestamp
++2026-08-13T00:00:00Z
-Timezone
++00:00
-Calendar
+Gregorian
-Precision
+day
 Before
 After
@@ Property / Collection date: 13 August 2026 / rank @@
+Normal rank
@@ Property / Linked ICD 10 @@
+D68.2
@@ Property / Linked ICD 10: D68.2 / rank @@
+Normal rank

Latest revision as of 05:03, 13 August 2026

Congenital deficiencies of fibrinogen are coagulation disorders characterised by bleeding symptoms ranging from mild to severe resulting from reduced quantity and/or quality of circulating fibrinogen. Afibrinogenaemia (complete absence of fibrinogen) and hypofibrinogenaemia (reduced plasma fibrinogen concentration) correspond to quantitative anomalies of fibrinogen while dysfibrinogenaemia corresponds to a functional anomaly of fibrinogen. Hypo- and dysfibrinogenaemia may be frequently combined (hypodysfibrinogenaemia).

Language	Label	Description	Also known as
default for all languages	3B14.0
English	Hereditary deficiency of factor I	Congenital deficiencies of fibrinogen are coagulation disorders characterised by bleeding symptoms ranging from mild to severe resulting from reduced quantity and/or quality of circulating fibrinogen. Afibrinogenaemia (complete absence of fibrinogen) and hypofibrinogenaemia (reduced plasma fibrinogen concentration) correspond to quantitative anomalies of fibrinogen while dysfibrinogenaemia corresponds to a functional anomaly of fibrinogen. Hypo- and dysfibrinogenaemia may be frequently combined (hypodysfibrinogenaemia).