Cutaneous mastocytosis (Q39214): Difference between revisions
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A mastocitose cutânea é caracterizada pelo acúmulo e proliferação anormais de mastócitos cutâneos. A maioria dos tipos é isolada, mas a mastocitose cutânea pode ocorrer em associação com doença sistêmica. As formas clínicas incluem mastocitoma cutâneo, urticária pigmentosa (a forma mais frequente), mastocitose cutânea nodular pseudoxantomatosa, telangiectasia macular eruptiva perstans e mastocitose cutânea difusa. | |||||||||||||||
| description / en | description / en | ||||||||||||||
Cutaneous mastocytosis is characterised by abnormal accumulation and proliferation of cutaneous mast cells. Most types are isolated but cutaneous mastocytosis can occur in association with systemic disease. Clinical forms include cutaneous mastocytoma, urticaria pigmentosa (the most frequent form), pseudoxanthomatous nodular cutaneous mastocytosis, telangiectasia macularis eruptiva perstans and diffuse cutaneous mastocytosis. | |||||||||||||||
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| Property / Canonical URI: https://id.who.int/icd/entity/1300710062 / rank | |||||||||||||||
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CID11:2A21.1 | |||||||||||||||
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dki-india-2A21.1 | |||||||||||||||
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| Property / Knowledge Architect: https://pauloleads.com.br/cases-publicos/ / rank | |||||||||||||||
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13 August 2026
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| Property / Collection date: 13 August 2026 / rank | |||||||||||||||
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| Property / Linked ICD 10: C96.2 / rank | |||||||||||||||
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Latest revision as of 04:33, 13 August 2026
Cutaneous mastocytosis is characterised by abnormal accumulation and proliferation of cutaneous mast cells. Most types are isolated but cutaneous mastocytosis can occur in association with systemic disease. Clinical forms include cutaneous mastocytoma, urticaria pigmentosa (the most frequent form), pseudoxanthomatous nodular cutaneous mastocytosis, telangiectasia macularis eruptiva perstans and diffuse cutaneous mastocytosis.
| Language | Label | Description | Also known as |
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| default for all languages | 2A21.1 |
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| English | Cutaneous mastocytosis |
Cutaneous mastocytosis is characterised by abnormal accumulation and proliferation of cutaneous mast cells. Most types are isolated but cutaneous mastocytosis can occur in association with systemic disease. Clinical forms include cutaneous mastocytoma, urticaria pigmentosa (the most frequent form), pseudoxanthomatous nodular cutaneous mastocytosis, telangiectasia macularis eruptiva perstans and diffuse cutaneous mastocytosis. |
Statements
CID11:2A21.1
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dki-india-2A21.1
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Concluído
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13 August 2026
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