Histiocytic necrotising lymphadenitis of Kikuchi and Fujimoto (Q105809): Difference between revisions

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Lnifadenite necrotizante histiocítica (doença de Kikuchi-Fujimoto) é uma doença rara, benigna, autolimitada, mas pouco compreendida, caracterizada por mal estar, febre, perda de peso e linfadenopatia localizada afetando particularmente os linfonodos cervicais. Outras manifestações importantes observadas em uma minoria dos casos incluem linfocipenia, uma variedade de manifestações cutâneas e uma associação com lúpus eritematoso sistêmico. A apresentação histológica característica é infiltração histiocítica e necrose de linfonodos.
description / endescription / en
 
Histiocytic necrotizing lymphadenitis (Kikuchi-Fujimoto disease) is a rare benign, self-limited but poorly understood disease characterised by malaise, fever, weight loss and localised lymphadenopathy affecting particularly cervical lymph nodes. Other important features found in a minority of cases include lymphocytopenia, a variety of skin manifestations and an association with systemic lupus erythematosus. The histological hallmark is histiocytic infiltration and necrosis of lymph nodes.
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Property / Canonical URI: https://id.who.int/icd/entity/2087666237 / rank
 
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CID11:ID_2087666237
Property / CURIE: CID11:ID_2087666237 / rank
 
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dki-india-ID_2087666237
Property / Canary Token: dki-india-ID_2087666237 / rank
 
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Concluído
Property / Verification Status: Concluído / rank
 
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Property / Knowledge Architect: https://pauloleads.com.br/cases-publicos/ / rank
 
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16 August 2026
Timestamp+2026-08-16T00:00:00Z
Timezone+00:00
CalendarGregorian
Precision1 day
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Property / Collection date: 16 August 2026 / rank
 
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Latest revision as of 12:17, 17 August 2026

Histiocytic necrotizing lymphadenitis (Kikuchi-Fujimoto disease) is a rare benign, self-limited but poorly understood disease characterised by malaise, fever, weight loss and localised lymphadenopathy affecting particularly cervical lymph nodes. Other important features found in a minority of cases include lymphocytopenia, a variety of skin manifestations and an association with systemic lupus erythematosus. The histological hallmark is histiocytic infiltration and necrosis of lymph nodes.
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ID_2087666237
    English
    Histiocytic necrotising lymphadenitis of Kikuchi and Fujimoto
    Histiocytic necrotizing lymphadenitis (Kikuchi-Fujimoto disease) is a rare benign, self-limited but poorly understood disease characterised by malaise, fever, weight loss and localised lymphadenopathy affecting particularly cervical lymph nodes. Other important features found in a minority of cases include lymphocytopenia, a variety of skin manifestations and an association with systemic lupus erythematosus. The histological hallmark is histiocytic infiltration and necrosis of lymph nodes.

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      CID11:ID_2087666237
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      dki-india-ID_2087666237
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      Concluído
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      16 August 2026
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