Dehydrated hereditary stomatocytosis (Q104350): Difference between revisions

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Latest revision as of 10:12, 17 August 2026

Dehydrated hereditary stomatocytosis is a rare congenital haemolytic anaemia with a dominant inheritance pattern. It is usually well compensated (moderate anaemia, high reticulocyte count). Blood smears show a variable percentage of stomatocytes. The association of a macrocytosis and an increased mean cell haemoglobin concentration is highly evocative of DHS.

Language	Label	Description	Also known as
default for all languages	ID_799088159
English	Dehydrated hereditary stomatocytosis	Dehydrated hereditary stomatocytosis is a rare congenital haemolytic anaemia with a dominant inheritance pattern. It is usually well compensated (moderate anaemia, high reticulocyte count). Blood smears show a variable percentage of stomatocytes. The association of a macrocytosis and an increased mean cell haemoglobin concentration is highly evocative of DHS.