Necrobiotic xanthogranuloma (Q92409): Difference between revisions
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O xantogranuloma necrobiótico (XGN) é uma doença histiocítica multissistêmica rara envolvendo a pele na qual nódulos e placas xantomatosos infiltrados disseminados estão associados na maioria dos casos com paraproteinemia e uma variedade de distúrbios linfoproliferativos subjacentes, incluindo mieloma. O XGN difere da xantomatose difusa plana normolipidêmica, na qual as lesões cutâneas são palpavelmente infiltradas e elevadas, em vez de planas e difusas naquela necrobiose, e células gigantes de Touton estão presentes histologicamente. | |||||||||||||||
| description / en | description / en | ||||||||||||||
Necrobiotic xanthogranuloma (NXG) is a rare multisystem histiocytic disease involving the skin in which widespread infiltrated xanthomatous nodules and plaques are associated in the majority of cases with paraproteinaemia and a variety of underlying lymphoproliferative disorders including myeloma. NXG differs from diffuse normolipidaemic plane xanthomatosis in that the skin lesions are palpably infiltrated and elevated rather than flat and diffuse and in that necrobiosis and Touton giant cells are present histologically. | |||||||||||||||
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| Property / Canonical URI: https://id.who.int/icd/entity/2138563851 / rank | |||||||||||||||
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CID11:ID_2138563851 | |||||||||||||||
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dki-india-ID_2138563851 | |||||||||||||||
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| Property / Knowledge Architect: https://pauloleads.com.br/cases-publicos/ / rank | |||||||||||||||
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15 August 2026
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| Property / Collection date: 15 August 2026 / rank | |||||||||||||||
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Latest revision as of 07:33, 16 August 2026
Necrobiotic xanthogranuloma (NXG) is a rare multisystem histiocytic disease involving the skin in which widespread infiltrated xanthomatous nodules and plaques are associated in the majority of cases with paraproteinaemia and a variety of underlying lymphoproliferative disorders including myeloma. NXG differs from diffuse normolipidaemic plane xanthomatosis in that the skin lesions are palpably infiltrated and elevated rather than flat and diffuse and in that necrobiosis and Touton giant cells are present histologically.
| Language | Label | Description | Also known as |
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| default for all languages | ID_2138563851 |
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| English | Necrobiotic xanthogranuloma |
Necrobiotic xanthogranuloma (NXG) is a rare multisystem histiocytic disease involving the skin in which widespread infiltrated xanthomatous nodules and plaques are associated in the majority of cases with paraproteinaemia and a variety of underlying lymphoproliferative disorders including myeloma. NXG differs from diffuse normolipidaemic plane xanthomatosis in that the skin lesions are palpably infiltrated and elevated rather than flat and diffuse and in that necrobiosis and Touton giant cells are present histologically. |
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CID11:ID_2138563851
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dki-india-ID_2138563851
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Concluído
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15 August 2026
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