Purpura fulminans (Q87934): Difference between revisions
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Purpura fulminans é um transtorno trombótico rapidamente progressivo potencialmente fatal afetando principalmente neonatos e crianças, caracterizado por lesões cutâneas purpúricas e coagulação intravascular disseminada. As lesões são inicialmente máculas eritematosas bem demarcadas, desenvolvendo rapidamente áreas centrais irregulares de necrose hemorrágica negro-azulada, tornando-se dolorosas, escuras e elevadas, às vezes com formação de vesículas ou bolhas. As lesões posteriormente levam a lesão isquêmica endotelial irreversível com necrose gangrenosa. A púrpura fulminante pode progredir rapidamente para falência de múltiplos órgãos por oclusão trombótica de vasos sanguíneos pequenos e médios. Existem três formas classificadas por mecanismo desencadeante: neonatal, infecciosa aguda (a forma mais comum) e idiopática. | |||||||||||||||
| description / en | description / en | ||||||||||||||
Purpura fulminans is a life-threatening, rapidly progressive thrombotic disorder affecting mainly neonates and children, characterised by purpuric skin lesions and disseminated intravascular coagulation. The lesions are initially well-demarcated erythematous macules, rapidly developing irregular central areas of blue-black haemorrhagic necrosis, becoming painful, dark and raised, sometimes with vesicle or bulla formation. Lesions later lead to irreversible endothelial ischemic injury with gangrenous necrosis. Purpura fulminans may progress rapidly to multi-organ failure by thrombotic occlusion of small and medium-sized blood vessels. There are three forms classified by triggering mechanism: neonatal, acute infectious (the most common form), and idiopathic. | |||||||||||||||
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| Property / Canonical URI: https://id.who.int/icd/entity/1293848111 / rank | |||||||||||||||
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CID11:ID_1293848111 | |||||||||||||||
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dki-india-ID_1293848111 | |||||||||||||||
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| Property / Knowledge Architect: https://pauloleads.com.br/cases-publicos/ / rank | |||||||||||||||
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13 August 2026
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| Property / Collection date: 13 August 2026 / rank | |||||||||||||||
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Latest revision as of 13:59, 15 August 2026
Purpura fulminans is a life-threatening, rapidly progressive thrombotic disorder affecting mainly neonates and children, characterised by purpuric skin lesions and disseminated intravascular coagulation. The lesions are initially well-demarcated erythematous macules, rapidly developing irregular central areas of blue-black haemorrhagic necrosis, becoming painful, dark and raised, sometimes with vesicle or bulla formation. Lesions later lead to irreversible endothelial ischemic injury with gangrenous necrosis. Purpura fulminans may progress rapidly to multi-organ failure by thrombotic occlusion of small and medium-sized blood vessels. There are three forms classified by triggering mechanism: neonatal, acute infectious (the most common form), and idiopathic.
| Language | Label | Description | Also known as |
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| default for all languages | ID_1293848111 |
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| English | Purpura fulminans |
Purpura fulminans is a life-threatening, rapidly progressive thrombotic disorder affecting mainly neonates and children, characterised by purpuric skin lesions and disseminated intravascular coagulation. The lesions are initially well-demarcated erythematous macules, rapidly developing irregular central areas of blue-black haemorrhagic necrosis, becoming painful, dark and raised, sometimes with vesicle or bulla formation. Lesions later lead to irreversible endothelial ischemic injury with gangrenous necrosis. Purpura fulminans may progress rapidly to multi-organ failure by thrombotic occlusion of small and medium-sized blood vessels. There are three forms classified by triggering mechanism: neonatal, acute infectious (the most common form), and idiopathic. |
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CID11:ID_1293848111
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dki-india-ID_1293848111
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Concluído
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13 August 2026
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