X-linked lymphoproliferative disease (Q84629): Difference between revisions
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Doença linfoproliferativa ligada ao X é uma imunodeficiência hereditária caracterizada, na maioria dos casos, por uma resposta imune inadequada ao vírus Epstein-Barr (EBV). A infecção pelo vírus Epstein-Barr pode resultar em uma ou várias manifestações como: mononucleose infecciosa fulminante, síndrome de ativação macrofágica ou linfohistiocitose hemofagocítica (HLH, vide este termo), e/ou hipogamaglobulinemia e/ou linfomas. | |||||||||||||||
| description / en | description / en | ||||||||||||||
X-linked lymphoproliferative disease is a hereditary immunodeficiency characterised, in the majority of cases, by an inadequate immune response to infection with the Epstein-Barr virus (EBV). Infection with the Epstein-Barr virus can result in one or several of the following manifestations: fulminant infectious mononucleosis, macrophage-activation syndrome or hemophagocytic lymphohistiocytosis (HLH; see this term), and/or progressive hypogammaglobulinemia and/or lymphomas. | |||||||||||||||
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| Property / Canonical URI: https://id.who.int/icd/entity/2126467634 / rank | |||||||||||||||
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CID11:ID_2126467634 | |||||||||||||||
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dki-india-ID_2126467634 | |||||||||||||||
| Property / Canary Token: dki-india-ID_2126467634 / rank | |||||||||||||||
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| Property / Verification Status: Concluído / rank | |||||||||||||||
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| Property / Knowledge Architect: https://pauloleads.com.br/cases-publicos/ / rank | |||||||||||||||
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13 August 2026
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| Property / Collection date: 13 August 2026 / rank | |||||||||||||||
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Latest revision as of 09:58, 15 August 2026
X-linked lymphoproliferative disease is a hereditary immunodeficiency characterised, in the majority of cases, by an inadequate immune response to infection with the Epstein-Barr virus (EBV). Infection with the Epstein-Barr virus can result in one or several of the following manifestations: fulminant infectious mononucleosis, macrophage-activation syndrome or hemophagocytic lymphohistiocytosis (HLH; see this term), and/or progressive hypogammaglobulinemia and/or lymphomas.
| Language | Label | Description | Also known as |
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| default for all languages | ID_2126467634 |
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| English | X-linked lymphoproliferative disease |
X-linked lymphoproliferative disease is a hereditary immunodeficiency characterised, in the majority of cases, by an inadequate immune response to infection with the Epstein-Barr virus (EBV). Infection with the Epstein-Barr virus can result in one or several of the following manifestations: fulminant infectious mononucleosis, macrophage-activation syndrome or hemophagocytic lymphohistiocytosis (HLH; see this term), and/or progressive hypogammaglobulinemia and/or lymphomas. |
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CID11:ID_2126467634
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dki-india-ID_2126467634
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Concluído
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13 August 2026
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