{"entities":{"Q98287":{"pageid":88680,"ns":120,"title":"Item:Q98287","lastrevid":557461,"modified":"2026-08-16T14:41:03Z","type":"item","id":"Q98287","labels":{"mul":{"language":"mul","value":"ID_488822470"},"pt-br":{"language":"pt-br","value":"Acrooste\u00f3lise tipo dominante"},"en":{"language":"en","value":"Acroosteolysis, dominant type"}},"descriptions":{"pt-br":{"language":"pt-br","value":"O tipo dominante de acrooste\u00f3lise, ou s\u00edndrome de Hajdu-Cheney, \u00e9 uma doen\u00e7a muito rara, caracterizada por baixa estatura, falanges distais com desaparecimento progressivo e ossos do carpo apinhados. Pode-se observar falha na ossifica\u00e7\u00e3o das suturas cranianas, com ab\u00f3bada craniana espessada, seio frontal ausente, sela t\u00farcica alongada e impress\u00e3o basilar progressiva."},"en":{"language":"en","value":"Acroosteolysis dominant type, or Hajdu-Cheney syndrome is a very rare disorder characterised by short stature, progressively disappearing distal phalanges and crowded carpal bones. Failure of ossification of cranial sutures can be seen, with thickened cranial vault, absent frontal sinus, elongated sella turcica, and progressive basilar impression."}},"aliases":{},"claims":{"P68":[{"mainsnak":{"snaktype":"value","property":"P68","hash":"14e02a3243f61da83aa49ad746054948f74c03d7","datavalue":{"value":"https://id.who.int/icd/entity/488822470","type":"string"},"datatype":"url"},"type":"statement","id":"Q98287$19F46FE8-7454-4A9D-B55F-56CC035B19DA","rank":"normal"}],"P67":[{"mainsnak":{"snaktype":"value","property":"P67","hash":"9a0cab7502f3104115c820a1a85c9c1f0e81e0e6","datavalue":{"value":"CID11:ID_488822470","type":"string"},"datatype":"string"},"type":"statement","id":"Q98287$150DC143-31D8-40B1-91D3-DBFC9A2C01F1","rank":"normal"}],"P70":[{"mainsnak":{"snaktype":"value","property":"P70","hash":"8b1c14a12aead4d3de8c6531dc628321185a3e0a","datavalue":{"value":"dki-india-ID_488822470","type":"string"},"datatype":"string"},"type":"statement","id":"Q98287$D8AFFA1B-BB41-412F-A2D1-E07AD58051E1","rank":"normal"}],"P86":[{"mainsnak":{"snaktype":"value","property":"P86","hash":"a96031634b9f5dafddaf781bbba3adea6bb64ef4","datavalue":{"value":"Conclu\u00eddo","type":"string"},"datatype":"string"},"type":"statement","id":"Q98287$8B0CD176-9EDF-430F-BAF2-7A24A40803A6","rank":"normal"}],"P78":[{"mainsnak":{"snaktype":"value","property":"P78","hash":"5f9b5be68b7400da549761cf15abfdbc4d1e075b","datavalue":{"value":"https://pauloleads.com.br/cases-publicos/","type":"string"},"datatype":"url"},"type":"statement","id":"Q98287$C32102BC-5AAD-4870-A83B-589737028012","rank":"normal"}],"P80":[{"mainsnak":{"snaktype":"value","property":"P80","hash":"378ac503ed43f21e1f461d2823a6ad59da580514","datavalue":{"value":{"time":"+2026-08-15T00:00:00Z","timezone":0,"before":0,"after":0,"precision":11,"calendarmodel":"http://www.wikidata.org/entity/Q1985727"},"type":"time"},"datatype":"time"},"type":"statement","id":"Q98287$1997AF26-B152-400D-8EAE-F6A327EF459D","rank":"normal"}]},"sitelinks":{}}}}