{"entities":{"Q96869":{"pageid":87262,"ns":120,"title":"Item:Q96869","lastrevid":547225,"modified":"2026-08-16T12:54:00Z","type":"item","id":"Q96869","labels":{"mul":{"language":"mul","value":"ID_1296778126"},"pt-br":{"language":"pt-br","value":"Pitir\u00edase rubra pilar tipo I, adulto cl\u00e1ssica"},"en":{"language":"en","value":"Pityriasis rubra pilaris type I, classical adult"}},"descriptions":{"pt-br":{"language":"pt-br","value":"Forma mais comum e reconhec\u00edvel de pitir\u00edase rubra pilar. Apresenta-se como uma erup\u00e7\u00e3o eritematosa escamosa de r\u00e1pida evolu\u00e7\u00e3o que \u00e9 inicialmente folicular, mas tipicamente progride para eritrodermia, dentro da qual caracteristicamente permanecem pequenas ilhas de pele n\u00e3o envolvida. Sem tratamento, tende a resolver-se espontaneamente ap\u00f3s uma m\u00e9dia de tr\u00eas anos. Afeta igualmente os sexos com maior incid\u00eancia entre os 40 e os 60 anos de idade. A causa \u00e9 pouco compreendida, embora muta\u00e7\u00f5es de ganho de fun\u00e7\u00e3o no gene CARD14 tenham sido relacionadas a formas gen\u00e9ticas raras da doen\u00e7a."},"en":{"language":"en","value":"This is the most common and recognisable form of pityriasis rubra pilaris. It presents as a rapidly evolving scaly erythematous rash which is initially follicular but typically progresses to erythroderma, within which small islands of uninvolved skin characteristically remain. Untreated, it tends to resolve spontaneously after an average of three years. It affects the sexes equally with the highest incidence between 40 and 60 years of age. The cause is poorly understood though gain-of-function mutations in the CARD14 gene have been linked to rare genetic forms of the disease."}},"aliases":{},"claims":{"P68":[{"mainsnak":{"snaktype":"value","property":"P68","hash":"410b3a8954dcad7f370dc7ca9addb0aab77f8985","datavalue":{"value":"https://id.who.int/icd/entity/1296778126","type":"string"},"datatype":"url"},"type":"statement","id":"Q96869$D9837739-944B-4099-8A70-B0A5DFFB4F80","rank":"normal"}],"P67":[{"mainsnak":{"snaktype":"value","property":"P67","hash":"70214f9a04b9d05655f746475ff1dbd0967cda93","datavalue":{"value":"CID11:ID_1296778126","type":"string"},"datatype":"string"},"type":"statement","id":"Q96869$AC7028C1-7B4D-4BAF-8D67-F9F2A6EAC912","rank":"normal"}],"P70":[{"mainsnak":{"snaktype":"value","property":"P70","hash":"a2bddb1d4915675b6378b84136b59672d44be86b","datavalue":{"value":"dki-india-ID_1296778126","type":"string"},"datatype":"string"},"type":"statement","id":"Q96869$B3571AC4-9B5F-489D-BC21-E619160AD63E","rank":"normal"}],"P86":[{"mainsnak":{"snaktype":"value","property":"P86","hash":"a96031634b9f5dafddaf781bbba3adea6bb64ef4","datavalue":{"value":"Conclu\u00eddo","type":"string"},"datatype":"string"},"type":"statement","id":"Q96869$8101DE07-D3A0-4FC3-A122-430B009CCCFF","rank":"normal"}],"P78":[{"mainsnak":{"snaktype":"value","property":"P78","hash":"5f9b5be68b7400da549761cf15abfdbc4d1e075b","datavalue":{"value":"https://pauloleads.com.br/cases-publicos/","type":"string"},"datatype":"url"},"type":"statement","id":"Q96869$0263D970-F781-46D0-B1EA-C2C166740A1B","rank":"normal"}],"P80":[{"mainsnak":{"snaktype":"value","property":"P80","hash":"378ac503ed43f21e1f461d2823a6ad59da580514","datavalue":{"value":{"time":"+2026-08-15T00:00:00Z","timezone":0,"before":0,"after":0,"precision":11,"calendarmodel":"http://www.wikidata.org/entity/Q1985727"},"type":"time"},"datatype":"time"},"type":"statement","id":"Q96869$67B6D659-3455-4D3F-B828-AAD2702C8D7B","rank":"normal"}]},"sitelinks":{}}}}