{"entities":{"Q92906":{"pageid":83299,"ns":120,"title":"Item:Q92906","lastrevid":518544,"modified":"2026-08-16T08:01:39Z","type":"item","id":"Q92906","labels":{"mul":{"language":"mul","value":"ID_892873372"},"pt-br":{"language":"pt-br","value":"S\u00edndrome do tumor hamartoma PTEN"},"en":{"language":"en","value":"PTEN Hamartoma tumour syndrome"}},"descriptions":{"pt-br":{"language":"pt-br","value":"S\u00edndrome do tumor hamartoma PTEN (PHTS) \u00e9 caracterizada por m\u00faltiplos hamartomas que podem afetar v\u00e1rias \u00e1reas do corpo. Hamartoma \u00e9 uma malforma\u00e7\u00e3o semelhante a um tumor benigno, composta de c\u00e9lulas maduras e tecido normalmente encontrado na \u00e1rea afetada. A PHTS \u00e9 causada por muta\u00e7\u00f5es no gene PTEN. A PHTS inclui virtualmente todos os casos da s\u00edndrome de Cowden (tamb\u00e9m conhecida como s\u00edndrome do hamartoma m\u00faltiplo) e uma porcentagem de casos de s\u00edndrome de Bannayan-Riley-Ruvalcaba, s\u00edndrome de Proteus e s\u00edndrome semelhante a Proteus."},"en":{"language":"en","value":"The PTEN hamartoma tumour syndrome (PHTS) is characterised by multiple hamartomas that can affect various areas of the body. Hamartoma is a benign tumour-like malformations, composed of mature cells and tissue normally found in the affected area. PHTS is caused by mutations of the PTEN gene. PHTS includes virtually all cases of Cowden syndrome (also known as multiple hamartoma syndrome) and a percentage of cases of Bannayan-Riley-Ruvalcaba syndrome, Proteus syndrome and Proteus-like syndrome."}},"aliases":{},"claims":{"P68":[{"mainsnak":{"snaktype":"value","property":"P68","hash":"15d0a54cf9bbff1cdee2e2570408b459b857f071","datavalue":{"value":"https://id.who.int/icd/entity/892873372","type":"string"},"datatype":"url"},"type":"statement","id":"Q92906$E5EF6C39-257E-40FC-8E99-B8D47E5AA32F","rank":"normal"}],"P67":[{"mainsnak":{"snaktype":"value","property":"P67","hash":"556234dd28836cfa96ba873a446568dbf0c437e8","datavalue":{"value":"CID11:ID_892873372","type":"string"},"datatype":"string"},"type":"statement","id":"Q92906$CAE23578-9120-4E22-83DB-7398A0F05F08","rank":"normal"}],"P70":[{"mainsnak":{"snaktype":"value","property":"P70","hash":"da021de75974240fa2724b29cbd73108d2ecc88f","datavalue":{"value":"dki-india-ID_892873372","type":"string"},"datatype":"string"},"type":"statement","id":"Q92906$95458218-6E39-453A-A703-07E79F362EF0","rank":"normal"}],"P86":[{"mainsnak":{"snaktype":"value","property":"P86","hash":"a96031634b9f5dafddaf781bbba3adea6bb64ef4","datavalue":{"value":"Conclu\u00eddo","type":"string"},"datatype":"string"},"type":"statement","id":"Q92906$6615ECC9-BB54-440C-8629-A45994585F54","rank":"normal"}],"P78":[{"mainsnak":{"snaktype":"value","property":"P78","hash":"5f9b5be68b7400da549761cf15abfdbc4d1e075b","datavalue":{"value":"https://pauloleads.com.br/cases-publicos/","type":"string"},"datatype":"url"},"type":"statement","id":"Q92906$568297F0-1320-4954-A819-38734187313A","rank":"normal"}],"P80":[{"mainsnak":{"snaktype":"value","property":"P80","hash":"378ac503ed43f21e1f461d2823a6ad59da580514","datavalue":{"value":{"time":"+2026-08-15T00:00:00Z","timezone":0,"before":0,"after":0,"precision":11,"calendarmodel":"http://www.wikidata.org/entity/Q1985727"},"type":"time"},"datatype":"time"},"type":"statement","id":"Q92906$76D4327F-09BE-4B18-B5F8-70A2557AC9DB","rank":"normal"}]},"sitelinks":{}}}}