{"entities":{"Q92829":{"pageid":83222,"ns":120,"title":"Item:Q92829","lastrevid":517986,"modified":"2026-08-16T07:57:09Z","type":"item","id":"Q92829","labels":{"mul":{"language":"mul","value":"ID_1064918621"},"pt-br":{"language":"pt-br","value":"Xeroderma pigmentoso B"},"en":{"language":"en","value":"Xeroderma pigmentosum B"}},"descriptions":{"pt-br":{"language":"pt-br","value":"Xeroderma pigmentoso do grupo de complementa\u00e7\u00e3o B (XPB) \u00e9 um subtipo extremamente raro de xeroderma pigmentoso (XP), uma fotodermatose rara que predisp\u00f5e ao c\u00e2ncer de pele. Alguns pacientes com XPB apresentam manifesta\u00e7\u00f5es cl\u00e1ssicas de XP de gravidade vari\u00e1vel (fotossensibilidade da pele com queima\u00e7\u00e3o e sardas, tumores de pele e olhos) e anormalidades neurol\u00f3gicas leves, enquanto outros combinam manifesta\u00e7\u00f5es cl\u00e1ssicas de XP com manifesta\u00e7\u00f5es sist\u00eamicas e neurol\u00f3gicas da s\u00edndrome de Cockayne, como baixa estatura, perda auditiva neurossensorial bilateral e hiperreflexia (complexo XP/CS)."},"en":{"language":"en","value":"Xeroderma pigmentosum complementation group B (XPB) is an extremely rare subtype of xeroderma pigmentosum (XP), a rare photodermatosis predisposing to skin cancers. Some XPB patients present with classic XP features of varying severity (photosensitivity of skin with burning and freckling, skin and eye tumours) and mild neurological abnormalities, while others combine classical XP features with systemic and neurological manifestations of Cockayne syndrome such as short stature, bilateral sensorineural hearing loss and hyperreflexia (XP/CS complex)."}},"aliases":{},"claims":{"P68":[{"mainsnak":{"snaktype":"value","property":"P68","hash":"6bce7f108469e8f52e2c3c68084f57dee58bf5c8","datavalue":{"value":"https://id.who.int/icd/entity/1064918621","type":"string"},"datatype":"url"},"type":"statement","id":"Q92829$8D56A3A9-DF48-4F23-A2AB-E267AD8923C1","rank":"normal"}],"P67":[{"mainsnak":{"snaktype":"value","property":"P67","hash":"79426bc65321328c63b85589a53a25509db83a13","datavalue":{"value":"CID11:ID_1064918621","type":"string"},"datatype":"string"},"type":"statement","id":"Q92829$A6B74813-4B01-49BC-90B1-A917C5982692","rank":"normal"}],"P70":[{"mainsnak":{"snaktype":"value","property":"P70","hash":"7b4ca139f15c154f981ee91d1641b05e78e6614e","datavalue":{"value":"dki-india-ID_1064918621","type":"string"},"datatype":"string"},"type":"statement","id":"Q92829$3B012BA5-1531-42FA-BCB7-8579DC05E00A","rank":"normal"}],"P86":[{"mainsnak":{"snaktype":"value","property":"P86","hash":"a96031634b9f5dafddaf781bbba3adea6bb64ef4","datavalue":{"value":"Conclu\u00eddo","type":"string"},"datatype":"string"},"type":"statement","id":"Q92829$6426F56C-FECC-47B1-AFF6-ADEA198F896A","rank":"normal"}],"P78":[{"mainsnak":{"snaktype":"value","property":"P78","hash":"5f9b5be68b7400da549761cf15abfdbc4d1e075b","datavalue":{"value":"https://pauloleads.com.br/cases-publicos/","type":"string"},"datatype":"url"},"type":"statement","id":"Q92829$B335BEFE-2EBC-43D4-BA1F-728FB1772B52","rank":"normal"}],"P80":[{"mainsnak":{"snaktype":"value","property":"P80","hash":"378ac503ed43f21e1f461d2823a6ad59da580514","datavalue":{"value":{"time":"+2026-08-15T00:00:00Z","timezone":0,"before":0,"after":0,"precision":11,"calendarmodel":"http://www.wikidata.org/entity/Q1985727"},"type":"time"},"datatype":"time"},"type":"statement","id":"Q92829$56517BB4-C5A0-443F-A139-B9D85F3FEA28","rank":"normal"}]},"sitelinks":{}}}}