{"entities":{"Q92039":{"pageid":82432,"ns":120,"title":"Item:Q92039","lastrevid":512277,"modified":"2026-08-16T07:11:41Z","type":"item","id":"Q92039","labels":{"mul":{"language":"mul","value":"ID_1367362159"},"pt-br":{"language":"pt-br","value":"Talassemia falciforme com crise com febre"},"en":{"language":"en","value":"Sickle cell thalassaemia with crisis with fever"}},"descriptions":{"pt-br":{"language":"pt-br","value":"Doen\u00e7a causada por uma muta\u00e7\u00e3o gen\u00e9tica da c\u00e9lula falciforme (HbS) de um progenitor e uma muta\u00e7\u00e3o da talassemia do outro progenitor. Esta doen\u00e7a \u00e9 caracterizada por hem\u00e1cias anormais r\u00edgidas em forma de foice e produ\u00e7\u00e3o anormal da cadeia beta em uma mol\u00e9cula de hemoglobina, crises e febre. Essa doen\u00e7a pode apresentar-se com palidez, icter\u00edcia, febre, sobrecarga de ferro, fadiga, ou falta de ar. A confirma\u00e7\u00e3o \u00e9 feita pela identifica\u00e7\u00e3o de muta\u00e7\u00f5es por testagem gen\u00e9tica."},"en":{"language":"en","value":"A disease caused by genetically inherited sickle cell (HbS) mutation from one parent and a thalassemia mutation from the other parent. This disease is characterised by abnormal rigid sickle-shaped red blood cells and abnormal production of the beta chain in a haemoglobin molecule, crisis and, fever. This disease may present with pallor, jaundice, fever, iron overload, fatigue, or shortness of breath. Confirmation is by identification of mutations through genetic testing."}},"aliases":{},"claims":{"P68":[{"mainsnak":{"snaktype":"value","property":"P68","hash":"45b68042eb35c7b6d72cce8fbd144e67aec13ab3","datavalue":{"value":"https://id.who.int/icd/entity/1367362159","type":"string"},"datatype":"url"},"type":"statement","id":"Q92039$E4D31F0E-370C-4F3C-BD8F-7F6FD099B5DB","rank":"normal"}],"P67":[{"mainsnak":{"snaktype":"value","property":"P67","hash":"0f0ed8c1d0db5187b134923d6430ae8e8348dbed","datavalue":{"value":"CID11:ID_1367362159","type":"string"},"datatype":"string"},"type":"statement","id":"Q92039$88CB0577-DB41-4CAB-BB69-C1874CD841B7","rank":"normal"}],"P70":[{"mainsnak":{"snaktype":"value","property":"P70","hash":"01ebac5f59a17247d3ee5f116c6cd8720d31fb5a","datavalue":{"value":"dki-india-ID_1367362159","type":"string"},"datatype":"string"},"type":"statement","id":"Q92039$14A5FF46-1DF0-43AD-929C-89A76B2DA05B","rank":"normal"}],"P86":[{"mainsnak":{"snaktype":"value","property":"P86","hash":"a96031634b9f5dafddaf781bbba3adea6bb64ef4","datavalue":{"value":"Conclu\u00eddo","type":"string"},"datatype":"string"},"type":"statement","id":"Q92039$33E69AB6-E67D-4957-B3A6-C23C59FC115F","rank":"normal"}],"P78":[{"mainsnak":{"snaktype":"value","property":"P78","hash":"5f9b5be68b7400da549761cf15abfdbc4d1e075b","datavalue":{"value":"https://pauloleads.com.br/cases-publicos/","type":"string"},"datatype":"url"},"type":"statement","id":"Q92039$70C2DDFC-6243-4820-BBB1-3683485F2FE6","rank":"normal"}],"P80":[{"mainsnak":{"snaktype":"value","property":"P80","hash":"378ac503ed43f21e1f461d2823a6ad59da580514","datavalue":{"value":{"time":"+2026-08-15T00:00:00Z","timezone":0,"before":0,"after":0,"precision":11,"calendarmodel":"http://www.wikidata.org/entity/Q1985727"},"type":"time"},"datatype":"time"},"type":"statement","id":"Q92039$4920E673-355D-43C6-9B5B-9C48B6A32A7E","rank":"normal"}]},"sitelinks":{}}}}