{"entities":{"Q91543":{"pageid":81936,"ns":120,"title":"Item:Q91543","lastrevid":509153,"modified":"2026-08-15T18:34:01Z","type":"item","id":"Q91543","labels":{"mul":{"language":"mul","value":"ID_1884871565"},"pt-br":{"language":"pt-br","value":"Parkinsonismo devido a neurodegenera\u00e7\u00e3o com ac\u00famulo cerebral de ferro (NBIA)"},"en":{"language":"en","value":"Parkinsonism due to Neurodegeneration with brain iron accumulation NBIA"}},"descriptions":{"pt-br":{"language":"pt-br","value":"Parkinsonismo pode ocorrer na neurodegenera\u00e7\u00e3o com ac\u00famulo cerebral de ferro (NBIA), que se refere a transtornos caracterizados por uma deposi\u00e7\u00e3o excessiva de ferro no c\u00e9rebro - especialmente nos g\u00e2nglios da base. Apenas dois transtornos, isto \u00e9, neuroferritinopatia e aceruloplasminemia, s\u00e3o transtornos do metabolismo do ferro no SNC. Em outros transtornos, como a neurodegenera\u00e7\u00e3o relacionada a PANK2 (anteriormente chamada de S\u00edndrome de Hallervorden Spatz), o papel exato do ferro para causar a degenera\u00e7\u00e3o n\u00e3o \u00e9 claro."},"en":{"language":"en","value":"Parkinsonism may occur in Neurodegeneration with brain iron accumulation(NBIA) that refers to disorders characterised by an excessive iron deposition in the brain-especially the basal ganglia. Only two disorders i.e. neuroferritinopathy and aceruloplasminemia are disorders of CNS iron metabolism. In others disorders such as PANK2 related Neurodegeneration-previously called Hallervorden Spatz Syndrome the exact role of iron in causing the degeneration is unclear."}},"aliases":{},"claims":{"P68":[{"mainsnak":{"snaktype":"value","property":"P68","hash":"5f34adc70b791cf186c923e93aa79f7c59a3ab70","datavalue":{"value":"https://id.who.int/icd/entity/1884871565","type":"string"},"datatype":"url"},"type":"statement","id":"Q91543$32D3AA47-E625-4BFA-9977-94302AC49D54","rank":"normal"}],"P67":[{"mainsnak":{"snaktype":"value","property":"P67","hash":"9fe9977fb22c3601d3bb40a4d9ee32d2e5cc5e1b","datavalue":{"value":"CID11:ID_1884871565","type":"string"},"datatype":"string"},"type":"statement","id":"Q91543$8018B10C-D8F4-455F-93CE-69C4DA19880B","rank":"normal"}],"P70":[{"mainsnak":{"snaktype":"value","property":"P70","hash":"e5ead0faaec8e0e1d63d6b2908918e34c9d3894c","datavalue":{"value":"dki-india-ID_1884871565","type":"string"},"datatype":"string"},"type":"statement","id":"Q91543$CA653AAE-EC32-46B5-8373-3254C37C822D","rank":"normal"}],"P86":[{"mainsnak":{"snaktype":"value","property":"P86","hash":"a96031634b9f5dafddaf781bbba3adea6bb64ef4","datavalue":{"value":"Conclu\u00eddo","type":"string"},"datatype":"string"},"type":"statement","id":"Q91543$EA95E5BA-17F2-4C0C-93D6-F2C8C90A292D","rank":"normal"}],"P78":[{"mainsnak":{"snaktype":"value","property":"P78","hash":"5f9b5be68b7400da549761cf15abfdbc4d1e075b","datavalue":{"value":"https://pauloleads.com.br/cases-publicos/","type":"string"},"datatype":"url"},"type":"statement","id":"Q91543$0C0F467B-240B-49CD-9108-BA2F8F03FE10","rank":"normal"}],"P80":[{"mainsnak":{"snaktype":"value","property":"P80","hash":"92b8222fcbb75718504f915073a3f43bd4003d18","datavalue":{"value":{"time":"+2026-08-13T00:00:00Z","timezone":0,"before":0,"after":0,"precision":11,"calendarmodel":"http://www.wikidata.org/entity/Q1985727"},"type":"time"},"datatype":"time"},"type":"statement","id":"Q91543$D492EC45-8605-478F-B9B8-84C319CD6DB4","rank":"normal"}]},"sitelinks":{}}}}