{"entities":{"Q90771":{"pageid":81164,"ns":120,"title":"Item:Q90771","lastrevid":503583,"modified":"2026-08-15T17:45:40Z","type":"item","id":"Q90771","labels":{"mul":{"language":"mul","value":"ID_83824621"},"pt-br":{"language":"pt-br","value":"Miopatia com corpos esferoides"},"en":{"language":"en","value":"Spheroid body myopathy"}},"descriptions":{"pt-br":{"language":"pt-br","value":"A miopatia com corpos esfer\u00f3ides \u00e9 uma doen\u00e7a rara classificada no grupo das miopatias cong\u00eanitas como um dist\u00farbio neuromuscular relacionado \u00e0 desmina, apresentando origem autoss\u00f4mica dominante com in\u00edcio dos sintomas na fase adulta. A bi\u00f3psia muscular revela corpos citoplasm\u00e1ticos esfer\u00f3ides caracter\u00edsticos."},"en":{"language":"en","value":"Spheroid body myopathy is a rare illness classified in the group of the congenital myopathies as a desmin-related neuromuscular disorder, presenting dominant autosomical origin with the beginning of the symptoms in the adult phase. Muscle biopsy discloses characteristic spheroid cytoplasmic bodies."}},"aliases":{},"claims":{"P68":[{"mainsnak":{"snaktype":"value","property":"P68","hash":"29f07676f5aca363f40c165345cfe9b80e4823e6","datavalue":{"value":"https://id.who.int/icd/entity/83824621","type":"string"},"datatype":"url"},"type":"statement","id":"Q90771$809AACA3-5655-4BD2-BBE5-FDB95A99E610","rank":"normal"}],"P67":[{"mainsnak":{"snaktype":"value","property":"P67","hash":"044f56580d1fe3a249233b07071623492645c211","datavalue":{"value":"CID11:ID_83824621","type":"string"},"datatype":"string"},"type":"statement","id":"Q90771$6D6FBDCE-D244-47A9-9948-A124DA4FADA2","rank":"normal"}],"P70":[{"mainsnak":{"snaktype":"value","property":"P70","hash":"1a4993317e35b2dd33f26abe741014f7136e126c","datavalue":{"value":"dki-india-ID_83824621","type":"string"},"datatype":"string"},"type":"statement","id":"Q90771$7E618F51-6BA9-4D25-A7D4-6DE9CBC93D85","rank":"normal"}],"P86":[{"mainsnak":{"snaktype":"value","property":"P86","hash":"a96031634b9f5dafddaf781bbba3adea6bb64ef4","datavalue":{"value":"Conclu\u00eddo","type":"string"},"datatype":"string"},"type":"statement","id":"Q90771$DCCEC1CC-D11C-4A28-8277-1CA9F6F938A8","rank":"normal"}],"P78":[{"mainsnak":{"snaktype":"value","property":"P78","hash":"5f9b5be68b7400da549761cf15abfdbc4d1e075b","datavalue":{"value":"https://pauloleads.com.br/cases-publicos/","type":"string"},"datatype":"url"},"type":"statement","id":"Q90771$8012D614-7B1F-43FF-8B4C-49E14FD30B33","rank":"normal"}],"P80":[{"mainsnak":{"snaktype":"value","property":"P80","hash":"92b8222fcbb75718504f915073a3f43bd4003d18","datavalue":{"value":{"time":"+2026-08-13T00:00:00Z","timezone":0,"before":0,"after":0,"precision":11,"calendarmodel":"http://www.wikidata.org/entity/Q1985727"},"type":"time"},"datatype":"time"},"type":"statement","id":"Q90771$DFE2AE00-08E4-47EB-AD91-650CCA8F1F10","rank":"normal"}]},"sitelinks":{}}}}