{"entities":{"Q90414":{"pageid":80804,"ns":120,"title":"Item:Q90414","lastrevid":500968,"modified":"2026-08-15T17:23:18Z","type":"item","id":"Q90414","labels":{"mul":{"language":"mul","value":"ID_447667859"},"pt-br":{"language":"pt-br","value":"Hipoplasia pontocerebelar tipo 4"},"en":{"language":"en","value":"Pontocerebellar hypoplasia type 4"}},"descriptions":{"pt-br":{"language":"pt-br","value":"Hipoplasia pontocerebelar tipo 4 \u00e9 uma forma muito rara de hipoplasia pontocerebelar caracterizada por in\u00edcio pr\u00e9-natal de polidr\u00e2mnio e contraturas seguidas por hipertonia, cl\u00f4nus grave, hipoventila\u00e7\u00e3o prim\u00e1ria levando a uma morte p\u00f3s-natal precoce."},"en":{"language":"en","value":"Pontocerebellar hypoplasia type 4 is a very rare form of pontocerebellar hypoplasia characterised by prenatal onset of polyhydramnios and contractures followed by hypertonia, severe clonus, primary hypoventilation leading to an early postnatal death."}},"aliases":{},"claims":{"P68":[{"mainsnak":{"snaktype":"value","property":"P68","hash":"e2718fa77d1ff9109820408dd4f27b5f88171049","datavalue":{"value":"https://id.who.int/icd/entity/447667859","type":"string"},"datatype":"url"},"type":"statement","id":"Q90414$9D36E1F6-4606-4BAA-B0EA-3783B1A000D1","rank":"normal"}],"P67":[{"mainsnak":{"snaktype":"value","property":"P67","hash":"b1763799b88a02592f7e46b5bb503c835fe5dbca","datavalue":{"value":"CID11:ID_447667859","type":"string"},"datatype":"string"},"type":"statement","id":"Q90414$8D90EED5-3838-4DD0-BD6D-19B9EB030DB5","rank":"normal"}],"P70":[{"mainsnak":{"snaktype":"value","property":"P70","hash":"ed013b051ce9c620d428de8e451eb187a55af00e","datavalue":{"value":"dki-india-ID_447667859","type":"string"},"datatype":"string"},"type":"statement","id":"Q90414$4574FB0D-F649-42E4-AFB5-8C5D5B4B901E","rank":"normal"}],"P86":[{"mainsnak":{"snaktype":"value","property":"P86","hash":"a96031634b9f5dafddaf781bbba3adea6bb64ef4","datavalue":{"value":"Conclu\u00eddo","type":"string"},"datatype":"string"},"type":"statement","id":"Q90414$EB0C279B-67EA-4F98-A71B-0BB6235521D2","rank":"normal"}],"P78":[{"mainsnak":{"snaktype":"value","property":"P78","hash":"5f9b5be68b7400da549761cf15abfdbc4d1e075b","datavalue":{"value":"https://pauloleads.com.br/cases-publicos/","type":"string"},"datatype":"url"},"type":"statement","id":"Q90414$28679943-2095-40C6-B458-4A9B87899E51","rank":"normal"}],"P80":[{"mainsnak":{"snaktype":"value","property":"P80","hash":"92b8222fcbb75718504f915073a3f43bd4003d18","datavalue":{"value":{"time":"+2026-08-13T00:00:00Z","timezone":0,"before":0,"after":0,"precision":11,"calendarmodel":"http://www.wikidata.org/entity/Q1985727"},"type":"time"},"datatype":"time"},"type":"statement","id":"Q90414$B50E9CF3-A54B-41CB-BC7F-C8E66863654D","rank":"normal"}]},"sitelinks":{}}}}